Volume 17

Journal of Cystic Fibrosis

Volume 17

1

Let's talk about sex: Behaviors, experience and health care utilization in young women with CF

Heltshe, Sonya L., Taylor-Cousar, Jennifer L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 125 KB

english, 2018

2

News

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 243 KB

english, 2018

3

New directions on lung clearance index variability and feasibility

O’Neill, Katherine, Saunders, Clare

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 165 KB

english, 2018

4

News

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 345 KB

english, 2018

5

Editorial Board

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 463 KB

english, 2018

6

WS13.3 The impact of pain on physiotherapy care in cystic fibrosis

Meneghini, G., Meschi, A., Cazzarolli, C., Franceschetti, C., Dal Pra’, S., Tomezzoli, S., D'Orazio, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

7

WS08.1 The utility of oxygen uptake efficiency as a marker of aerobic fitness in children with cystic fibrosis

Tomlinson, O.W., Barker, A.R., Chubbock, L.V., Stevens, D., Saynor, Z.L., Oades, P.J., Williams, C.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

8

P005 Two years of newborn screening for cystic fibrosis in Turkey: Cukurova experience

Altintas, D.U., Sasihuseyinoglu, A.S., Bisgin, A., Dogruel, D., Yilmaz, M., Serbes, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

9

P016 Late diagnosis of CF - the possible hazard for the family

Petrova, G., Hinkov, G., Stoeva, N., Kostadinov, D., Miteva, D., Hristova, V., Naydenova, A., Perenovska, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

10

P082 Inhaled dry powder colistin (Colobreathe ® ) in regular cystic fibrosis therapy in patients from a centre in Sofia

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

11

P150 Reasons for non-compliance with cardiopulmonary exercise testing in cystic fibrosis

Trott, J., Tomlinson, O., Bowhay, B., Williams, C., Withers, N., Oades, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

12

P155 Feasibility of using online video calling to engage patients in the management of cystic fibrosis

Tomlinson, O.W., Trott, J., Bowhay, B., Shelley, J., Enderby, B., Chauhan, R., Sheldon, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 64 KB

english, 2018

13

P186 Children in Bulgaria with mainly gastrointestinal onset of CF have worse nutritional results, despite being diagnosed earlier

Baicheva, M., Yaneva, P., Hadjijski, P., Kofinova, D., Petrova, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

14

P213 The heart in CF - three cases from Bulgaria

Naydenov, S., Perenovska, P., Miteva, D., Petrova, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

15

P272 The health status of mothers with CF in Bulgaria

Petrova, G., Hinkov, G., Stoeva, N., Hristova, V., Yaneva, N., Naydenova, A., Savov, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

16

WS06.3 A novel approach based on low field nuclear magnetic resonance to monitor lung functionality and inflammation in cystic fibrosis patients

Abrami, M., Maschio, M., Conese, M., Confalonieri, M., Di Gioia, S., Dapas, B., Tonon, F., Farra, R., Grassi, M., Grassi, G., Gerin, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

17

WS11.1 Alginate oligomers as novel therapies to treat life-threatening pseudomonal multidrug resistant bacterial infections

Oakley, J.L., Pritchard, M.F., Powell, L.C., Forton, J.M., Doull, I., Rye, P.D., Hill, K.E., Thomas, D.W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

18

P019 Advanced molecular dynamics simulations for understanding the functions and dysfunctions of the CFTR channel

Elbahnsi, A., Pietrucci, F., Hoffmann, B., Lehn, P., Décout, J.-L., Mornon, J.-P., Callebaut, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

19

P072 Taxonomic and functional microbial signatures of cystic fibrosis lung disease

Bacci, G., Armanini, F., Taccetti, G., Lucidi, V., Dolce, D., Fiscarelli, E., Negroni, A., Morelli, P., Casciaro, R., Segata, N., Mengoni, A., Bevivino, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

20

P078 Activity of liposomal loaded azithromycin against cystic fibrosis clinical respiratory isolates

Mairs, R., Dallal Bashi, Y., Elborn, J.S., Gilpin, D.F., Kett, V., Tunney, M.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

21

WS01.1 A phase 3, 2-part, single-arm study of ivacaftor treatment in patients

Rosenfeld, M., Wainwright, C., Mckee, C., Higgins, M., Wang, L., Campbell, D., Tian, S., Schneider, J., Cunningham, S., Davies, J.C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 263 KB

english, 2018

22

WS01.2 Phase 2 initial results evaluating PTI-428, a novel CFTR amplifier, in patients with cystic fibrosis

Flume, P., Sawicki, G., Pressler, T., Schwarz, C., Fajac, I., Layish, D., Bialek, P., Wilson, S., Kang, L., Mclaughlin, B., Scafidi, S., Lee, P.-S., Gilmartin, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 281 KB

english, 2018

23

WS01.3 Translational read-through of CFTR nonsense mutations and inducement of cystic fibrosis transmembrane conductance regulator (CFTR) function by ELX-02 treatment

Rowe, S.M., Mutyam, V., Alroy, I., Huertas, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

24

WS01.4 GLPG2222 in subjects with cystic fibrosis and the F508del/Class III mutation on stable treatment with ivacaftor: results from a phase II study (ALBATROSS)

Bell, S., De Boeck, K., Drevinek, P., Plant, B., Barry, P., Elborn, S., de Kock, H., Loyau, S., Muller, K., Vandebriel, L., Kanters, D., Van de Steen, O., Conrath, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

25

WS01.5 A 2-part, phase 3 single-arm study to evaluate the safety and pharmacokinetics (PK) of lumacaftor/ivacaftor (LUM/IVA) combination therapy in patients (pts) aged 2 to 5 years with cystic fibrosis (CF) homozygous for the F508del- CFTR mutation

Mcnamara, J., Mccolley, S.A., Owen, C.A., Liu, F., Tian, S., Waltz, D., Marigowda, G., Sawicki, G.S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 72 KB

english, 2018

26

WS01.6 Preliminary safety and efficacy of triple combination CFTR modulator regimens in cystic fibrosis

Davies, J.C., Colombo, C., Tullis, E., Mckee, C., Desouza, C., Waltz, D., Savage, J., Fisher, M., Shilling, R., Moskowitz, S., Robertson, S., Tian, S., Taylor-Cousar, J.L., Rowe, S.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

27

WS15.2 R334W CFTR, a severely compromised chloride conductance mutant, retains its bicarbonate conductance and responds to the corrector combination, C4 + C18

Boinot, C., Wang, H., Sabirzhanova, I., Cebotaru, C., Guggino, W., Cebotaru, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 72 KB

english, 2018

28

WS05.2 Impact of tobacco smoke exposure on pulmonary function in paediatric cystic fibrosis patients

Oates, G.R., Zhu, A., Stepanikova, I., Thomas, L., Gamble, S., Mims, C., Gutierrez, H., Harris, W.T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

29

P073 Use of qPCR to analyse changes in total bacterial and Pseudomonas aeruginosa load in cystic fibrosis patients when clinically stable and during exacerbations

MCGettigan, C., Spence, C., Lee, A.J., Sherrard, L., Johnston, E., Einarsson, G.G., Elborn, J.S., Downey, D., Muhlebach, M., Boucher, R., MCElvaney, G., Michelle, M., Lavelle, G., Tunney, M.M., Gilpin

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

30

WS09.1 Development of a CFTR mRNA therapy capable of treating lung disease in all CFTR patients

Smith, L., Karve, S., De Rosa, F., Kaza, N., Shei, R.-J., Stanford, D., Askew, K., Heartlein, M., Rowe, S., Mccauley, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

31

IPD2.01 Disease progression in patients with CF treated with ivacaftor: analyses of real-world data from the US and UK CF Registries

Volkova, N., Evans, J., Higgins, M., Campbell, D., Tian, S., Simard, C., Sewall, A., Nyangoma, S., Elbert, A., Marshall, B., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

32

IPD2.02 Real-world outcomes in patients with CF treated with ivacaftor: 2016 US and UK CF Registry analyses

Volkova, N., Evans, J., Higgins, M., Campbell, D., Tian, S., Simard, C., Sewall, A., Nyangoma, S., Elbert, A., Marshall, B., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

33

P020 Development of a 3D full thickness cystic fibrosis model on chip

Mazio, C., Scognamiglio, L.S., Casale, C., Imparato, G., Urciuolo, F., Netti, P.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

34

P035 Differential gene expression by Pseudomonas aeruginosa in response to bacteriophage infection

Brugha, R., Martin, I., Morales, S., Lehman, S., Alton, E., Davies, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

35

P090 In vitro susceptibility to ceftolozane/tazobactam in Pseudomonas aeruginosa isolates at an adult cystic fibrosis centre

Edwards, G., Smith, M., Downes, A., Cullen, M., Bright-Thomas, R.J., Jones, A.M., Barry, P.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

36

P197 FODMAP intake and gastrointestinal symptoms in cystic fibrosis - is there a relationship?

Tierney, A.C., Al-Helou, Z., King, S., Shepherd, S.J., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

37

WS11.5 Post-antibiotic effect of hypothiocyanite, lactoferrin and ALX-009 on clinical strains isolated from cystic fibrosis patients

Jubeau, L., Juarez Perez, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

38

WS12.1 Pioneering virtual reality technology for distraction therapy at the All Wales Adult CF Centre

Speight, L., Edwards, V., O'leary, C., Bridges, C., Hapgood, G., Jones, R., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

39

WS12.2 Supporting cystic fibrosis care at University Hospital Limerick (UHL) through eHealth

Murphy, N., Collins, L., Tierney, A., Linnane, B., Casserly, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

40

WS14.2 Phase 3 randomised controlled study of the efficacy and safety of inhaled mannitol in adults with cystic fibrosis

Amelina, E., Flume, P., Krasko, V., Carryer, B., Charlton, B., Leadbetter, J., Miller, J., Aitken, M.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

41

EPS5.03 Stenotrophomonas maltophilia and Achromobacter xylosoxidans in cystic fibrosis: epidemiology and lung disease progression

Bouhlel, L., Chiron, R., Degand, N., Godreuil, S., Caimmi, D., Bailly-Piccini, C., Leroy, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

42

EPS5.05 Epidemiology and phenotype of cystic fibrosis with residual function mutations in Italy

Salvatore, D., Padoan, R., Buzzetti, R., Amato, A., Giordani, B., Ferrari, G., Majo, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 74 KB

english, 2018

43

P003 Newborn screening for cystic fibrosis in Serbia: a pilot study

Grkovic, S., Minic, P., Radivojevic, D., Lalic, T., Sovtic, A., Djurisic, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 282 KB

english, 2018

44

P232 How the Socratic questioning method can be used by the cystic fibrosis multidisciplinary team to develop a deeper understanding of patients’ difficulties and aid decision making

Biggin, I.J., Phillips, S.K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

45

P233 Developing awareness of psychosocial issues for the cystic fibrosis multidisciplinary team - using the psychologist differently

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

46

P234 Transplant eligibility perceptions amongst a cystic fibrosis multidisciplinary team

Brockelsby, C., Frost, F., Griffiths, P., Greenwood, J., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

47

P235 The cost of caring: nursing experiences of palliation within cystic fibrosis care

Sumner, C., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 63 KB

english, 2018

48

P239 Pioneering virtual reality technology for transition at the All Wales Adult CF Centre

Speight, L., Prosser, A., O'leary, C., Edwards, V., Bridges, C., Hapgood, G., Jones, R., Ketchell, R., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

49

P240 Association between adherence to azithromycin and dornase alpha and lung function decline in adult cystic fibrosis (CF) patients: a two-year analysis

Popowicz, N., Wood, J., Mulrennan, S., Budgeon, C., Ryan, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

50

P036 Whole genome variant analysis and transposon sequencing provides insight into aztreonam resistance in cystic fibrosis Pseudomonas aeruginosa airway infection

Mclean, K., Holmes, E., Penewit, K., Waalkes, A., Ren, M., Harwood, R., Lee, S., Gasper, J., Manoil, C., Salipante, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

51

P084 Bacteriophage treatment of multidrug-resistant Pseudomonas aeruginosa pneumonia in a cystic fibrosis patient

Furr, C.-L.L., Lehman, S.M., Morales, S.P., Rosas, F.X., Gaidamaka, A., Bilinsky, I.P., Grint, P.C., Schooley, R.T., Aslam, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

52

WS08.2 Acute effects of combined exercise and oscillatory positive expiratory pressure therapy on sputum properties and lung diffusing capacity in cystic fibrosis: a randomised, controlled, crossover trial

Radtke, T., Böni, L., Bohnacker, P., Maggi-Bebba, M., Fischer, P., Kriemler, S., Benden, C., Dressel, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

53

EPS4.05 Determining the relationship between absolute quantification and relative abundance as determined by next generation sequencing

McGettigan, C., Johnston, E., Elborn, J.S., Lee, A.J., Sherrard, L., Damian, D., Einarsson, G.G., Spence, C., Muhlebach, M., Boucher, R., Mcelvaney, G., Murray, M., Lavelle, G., Tunney, M.M., Gilpin,

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

54

P089 Synergistic activities of an efflux pump inhibitor and antibiotics against Pseudomonas aeruginosa isolates from cystic fibrosis patients

Gbian, D.L., Omri, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

55

P201 Features of somatic growth of children with CF in different age periods in the Russian Federation

Maksimysheva, T., Kondratyeva, E., Voronkova, A., Melyanovskaya, Y., Sherman, V., Zhekayte, E., Chernyak, A., Nazarenko, L., Odinokova, O., Smirnova, I., Mukhacheva, V., Nikonova, V., Shabalova, L., G

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

56

P030 Modelled deposition of colistimethate sodium aerosol in the lungs of patients with cystic fibrosis using two different mesh nebulisers

Hull, D., Black, A., Vos, W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

57

P196 Breastfeeding and higher SES lead to better outcomes in children with CF

Faro, A., Elbert, A., Fink, A., Wu, R., Marshall, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

58

WS04.2 Azithromycin treatment of Pseudomonas aeruginosa infection potentiates IgY pulmonary protection in vivo

Thomsen, K., Larsen, S., Christophersen, L., Lerche, C., Høiby, N., Moser, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 76 KB

english, 2018

59

WS09.2 Developing scarless and permanent CFTR correction using CRISPRs

Duan, C., Xia, E., Hu, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 74 KB

english, 2018

60

WS09.3 Development of effective method for F508del mutation correction using CRISPR/Cas9

Smirnikhina, S., Anuchina, A., Adilgereeva, E., Kochergin-Nikitsky, K., Lavrov, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

61

WS09.4 Targeting αENaC with an epithelial RNAi trigger delivery platform for the treatment of cystic fibrosis

Bush, E.W., Nicholas, A., Pei, T., Kuipers, I., Cheng, W., Hamilton, H., Hegge, J., Li, X., Glebocka, A., Zhu, R., Chen, B., Kuehl, P., Schluep, T., Li, Z.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

62

WS09.6 The ENaC regulatory peptide SPX-101 is stable in CF sputum and functional regardless of CFTR mutation

Scott, D., Wu, B., Stuhlmiller, T., Sesma, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

63

WS10.1 Isolated non-visualisation of foetal gallbladder should be considered for the prenatal diagnosis of cystic fibrosis

Bergougnoux, A., Jouannic, J.-M., Verneau, F., Bienvenu, T., Gaitch, N., Raynal, C., Girodon, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 72 KB

english, 2018

64

IPD2.10 Observational study of glucose tolerance abnormalities in patients with cystic fibrosis homozygous for Phe508del CFTR treated by lumacaftor-ivacaftor

Misgault, B., Chatron, E., Durieu, I., Mely, L., Abely, M., Bounyar, L., Porzio, M., Weiss, L., Kessler, R., Kessler, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

65

P006 Advanced search for CFTR gene mutations in Russian CF patients

Petrova, N.V., Vasilyeva, T.A., Kashirskaya, N.Y., Kondratyeva, E.I., Voronkova, A.Y., Sherman, V.D., Ginter, E.K., Zinchenko, R.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

66

P203 Malnutrition in adolescent and adult patients with cystic fibrosis

Spirevska, L., Fustik, S., Jakovska, T., Zorcec, T., Stamatova, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

67

P249 Comparison of depression, burnout, caregiver burden and parent-child attitudes in cystic fibrosis and primary ciliary dyskinesia in children's mothers

Eyüboğlu, T.S. Şişmanlar, Gursoy, T. Ramaslı, Aslan, A.T., Emiralioglu, N., Pekcan, S., Buyukkaya, Z., Hangül, M., Kose, M., Soysal, S., Budakoglu, I.I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

68

P085 Synergistic activity of colistin in combination with N-acetylcysteine against colistin-resistant Acinetobacter baumannii grown in biofilms

Sergio, F., Pallecchi, L., Blasi, F., Aliberti, S., Pollini, S., Boncompagni, S., Di Maggio, T., Rossolini, G.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

69

P229 Round table meetings for parents of CF babies diagnosed through newborn screening

Tiesinga, A.M., Zwolsman, M.G., Rottier, B.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

70

P230 An attempt to reduce the psychological consequences of isolation during paediatric hospitalisations in cystic fibrosis centre

Borawska-Kowalczyk, U., Cichocka, A., Jeneralska, N., Witkowski, M., Grądzka, E., Sands, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

71

WS16.6 Human epididymis protein 4 (HE4) plasma levels inversely correlate with improved FEV 1 in cystic fibrosis patients under ivacaftor therapy as a new sensitive treatment efficacy biomarker

Nagy, B., Bene, Z., Fejes, Z., Heltshe, S.L., Ronan, N.J., Joseloff, E., Kappelmayer, J., Macek, M., Bell, S.C., Plant, B.J., Amaral, M.D., Balogh, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 79 KB

english, 2018

72

EPS2.05 Genotype/phenotype correlation in cystic fibrosis children with mutation 3272-16T > A

Furman, E.G., Shadrina, V.V., Krasovsky, S.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

73

P008 CFTR gene mutation spectrum peculiarities in Russian cystic fibrosis patients

Adyan, T., Krasovsky, S., Stepanova, A., Polyakov, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

74

WS03.4 Comparing abdominal symptoms in cystic fibrosis patients and healthy controls with a novel multimodal questionnaire (CF-Abd Score)

Jaudszus, A., Zeman, E., Michl, R., Lorenz, M., Beiersdorf, N., Tabori, H., Mainz, J.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

75

EPS1.02 Biochemical and biophysical properties of bronchial mucus from preschool children with cystic fibrosis

Ramsey, K., Hill, D., Markovetz, M., Garbarine, I., Kesimer, M., Boucher, R., Stick, S., Schultz, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 270 KB

english, 2018

76

IPD2.07 Retrospective observational study in cystic fibrosis patients homozygous for F508del treated with lumacaftor/ivacaftor in a compassionate use programme

Iacotucci, P., Carnovale, V., Blasi, F., Braggion, C., Castellani, C., Cipolli, M., Collura, M., Colombo, C., Lucidi, V., Minicucci, L., Manca, A., Magazzù, G., Ferrara, N.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

77

IPD2.13 Treatment with ivacaftor in CF patients with the G551D mutation is associated with improvement in cognition

Wilson, J., Allen-Graham, J., Talbot, A., Finlayson, F., Clark, D., Keating, D., Edgeworth, D., Williams, E., Kotsimbos, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

78

P132 A qualitative account of the first UK cystic fibrosis trust physiotherapy fellowship

Bass, R., Morrison, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 49 KB

english, 2018

79

EPS2.07 Intestinal current and nasal potential difference index cases: diagnostic features of subjects with CFTR-related disorder

Hyde, R., Gyulumyan, L., Alfeis, N., Tamm, S., Stanke, F., Dopfer, C., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

80

EPS6.01 Shaking it up: a look at our centre experience with high frequency chest wall oscillation (HFCWO)

Bridges, C., Carter, H., Ketchell, R.I., Lau, D., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

81

P190 Body composition changes in the first year of treatment with lumacaftor-ivacaftor in adults with severe cystic fibrosis lung disease

King, S.J., Williams, E., Allen-Graham, J., Finlayson, F., Button, B.M., Clark, D., Kotsimbos, T., Keating, D., Tierney, A.C., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

82

WS15.6 A phase 3, open-label study of tezacaftor/ivacaftor (TEZ/IVA) therapy: interim analysis of pooled safety, and efficacy in patients heterozygous for F508del-CFTR and a residual function mutation

Flume, P., Owen, C.A., Fischer Biner, R., Simard, C., Downey, D.G., Zhou, H., Lekstrom-Himes, J., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

83

P028 Riociguat for the treatment of adult Phe508del homozygous cystic fibrosis: efficacy data from the Phase II Rio-CF study

Taylor-Cousar, J.L., Tullis, E., Derichs, N., Davies, J.C., Nazareth, D., Downey, D., Rosenbluth, D., Fajac, I., Malfroot, A., Saunders, C., Short, C., Jensen, R., Solomon, G.M., Vermeulen, F., Willma

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

84

P121 Short-term effect of physiotherapy on Lung Clearance Index among patients with cystic fibrosis

Kouroukli, E., Hatziagorou, E., Parisi, M., Peftoulidou, P., Mouratidou, I.-C., Tsanakas, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

85

P236 Life coaching among young adults with cystic fibrosis - a qualitative study

Knudsen, K.B., Boisen, K.A., Katzenstein, T.L., Mortensen, L.H., Pressler, T., Skov, M., Jarden, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

86

P126 Bronchoscopy and airway clearance techniques in cystic fibrosis

Elidottir, H., Wallin, K., Hansen, C.R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

87

WS17.3 Functional characterisation and CFTR2 disease liability assignment of 48 missense variants

Raraigh, K.S., Han, S., Davis, E., Evans, T., Pellicore, M., Mccague, A., Joynt, A., Lu, Z., Atalar, M., Sharma, N., Sosnay, P.R., Cutting, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 78 KB

english, 2018

88

WS17.5 Nasal potential difference measurement increases the diagnostic yield in patients with equivocal first-line cystic fibrosis investigations: the experience of a large national CFTR diagnostic service

Simmonds, N.J., Pabary, R., Kohlhäufl, J., Waller, M., Alton, E.W., Davies, J.C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

89

WS19.2 The use of a questionnaire and continuous glucose monitoring to screen for hypoglycaemia in a cystic fibrosis clinic

Armaghanian, N., Taylor, N., Markovic, T.P., Brand-Miller, J.C., Bye, P.T., Graham, C., Steinbeck, K.S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

90

P211 Prevalence of low BMD, osteoporosis and DEXA scan attendance in the North Ireland Adult CF Centre: the relationship to current guidelines

Lynch, V., Gorman, C., Addy, C., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

91

EPS6.08 The effects of Orkambi therapy on muscle strength, function, body composition and quality of life in CF patients homozygous for CFTR- F508del

Reilly, C., Buckley, R., Kelly, S., O'shaughnessy, L., Landers, C., Mc Keown, C., Gallagher, C.G., Mc Kone, E.F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 49 KB

english, 2018

92

IPD1.03 Depression among parents of children with cystic fibrosis and its socioeconomic determinants

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 275 KB

english, 2018

93

P098 The “rare-exacerbator” status in adult cystic fibrosis patients

Gramegna, A., Sotgiu, G., Contarini, M., Aliberti, S., Saderi, L., Colombo, A., Vanoni, N., Amati, F., Pizzamiglio, G., Di Pasquale, M., Dellafiore, S., Pappalettera, M., Colombo, C., Castellani, C.,

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 78 KB

english, 2018

94

WS02.1 Epidemiology of nontuberculous mycobacteria infection in children and young people with cystic fibrosis: analysis of United Kingdom Cystic Fibrosis Trust Registry data

Brodlie, M., Gardner, A.I., Mcclenaghan, E., Saint, G.L., Mcnamara, P.S., Thomas, M.F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

95

WS02.2 Prevalence of nontuberculous mycobacteria in potable water

Stockwell, R.E., Leong, L.E.X., Wood, M.E., Sherrard, L.J., Carter, R., Tolson, C., Thomson, R.M., Rogers, G., Wainwright, C.E., Bell, S.C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

96

WS02.3 Antibody testing for Mycobacterium avium complex infection in cystic fibrosis patients

Ravnholt, C., Qvist, T., Pressler, T., Kolpen, M., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

97

WS02.5 Treatment success for eradication of pulmonary nontuberculous mycobacterial infections in a paediatric cystic fibrosis cohort

Hughes, D., Davenport, A., Carr, S.B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

98

WS03.1 Growth, body composition and lung function in pre-pubertal children with cystic fibrosis diagnosed via newborn screening, and comparison with a historical unscreened cohort

Owen, E., Fewtrell, M., Wallis, C., Williams, J.E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

99

WS03.3 Childhood nutritional status is a major factor determining lung function in adults with cystic fibrosis

Ashkenazi, M., Nathan, N., Sarouk, I., Bar Aluma, B.E., Dagan, A., Bezalel, Y., Vilozni, D., Efrati, O.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

100

WS03.6 A first approach for an evidence-based method to adjust PERT: in vivo validation of the in vitro model

Calvo-Lerma, J., Hulst, J., Boon, M., Masip, E., Fornés-Ferrer, V., Garriga, M., Colombo, C., Crespo, P., Roca, M., Woodcock, S., Van der Wiel, E., Claes, I., de Boeck, K., Ribes-Koninckx, C., MyCyFAP

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

101

WS04.1 Targeting IL-17-producing T-cells attenuates the severity of Pseudomonas aeruginosa lung infection

Lorè, N.I., Sipione, B., Melessike, M., Mertz, J.A., Kolls, J.K., Bragonzi, A., Cigana, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

102

WS04.3 Sodium influx modulates innate immune inflammation and metabolism in cystic fibrosis

Scambler, T., Wong, C., Pathak, S., Lara Reyna, S., Holbrook, J., Jarosz-Griffiths, H., Martinon, F., Savic, S., Peckham, D., McDermott, M.F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

103

WS04.4 Investigation of the CFTR-TGFβ 1 interaction regarding inflammatory effects in wildtype and CFTR-mutated human bronchial epithelial cells

Thomassen, J.C., Vohlen, C., Rietschel, E., van Koningsbruggen-Rietschel, S., Alejandre Alcazar, M.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

104

WS04.5 The effect of cysteamine and epigallocatechin gallate on hyperresponsive inflammation in cystic fibrosis

Holbrook, J.A., Scambler, T., Lara-Reyna, S., Wong, C., Jarosz-Griffiths, H., Savic, S., Peckham, D., McDermott, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

105

WS05.4 Clinical effectiveness results from the first interim analysis of the VOCAL study; an observational study of ivacaftor in patients with cystic fibrosis and selected non-G551D gating mutations

Castellani, C., Colombo, C., van der Ent, C.K., Simmonds, N.J., Kinnman, N., Hassan, M., DeSouza, C., Kaviya, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

106

WS05.5 Pregnancy outcome in women with cystic fibrosis and poor pulmonary function

Reynaud, Q., Poupon Bourdy, S., Rousset Jablonski, C., Lemonnier, L., Nove Josserand, R., Durupt, S., Touzet, S., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

107

WS05.6 Mortality outcomes related to multi-drug resistant organisms in cystic fibrosis lung transplant recipients: an International Society of Heart and Lung Transplantation (ISHLT) thoracic transplant Registry study

Benden, C., Lay, C., Law, N., Holm, A.M., Aslam, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

108

WS06.1 Monitoring cystic fibrosis lung disease in school-age children with computer tomography

Svedberg, M., Gustafsson, P., Sigurdsson, G.V., Lindblad, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

109

WS06.2 Interest of sequential expiratory chest computed tomography in monitoring lung disease of children with cystic fibrosis

Simon, S., Mittaine, M., Vial, J., Combelles, S., Gauthier, L., Brémont, F., Baunin, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

110

WS06.4 Lung ultrasound score and the relation with lung clearance index

Ciuca, I., Dediu, M., Tamas, L., Pop, L.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

111

WS06.5 A methodology to evaluate trapped gas using an open circuit Multiple Breath Nitrogen Washout (MBWN 2 ) device

Short, C., Saunders, C., Semple, T., Davies, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

112

WS07.1 Moving into the 21 st century with dietetic care - changing patient perceptions

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

113

WS07.6 At a loss: the failings of multi-agency working?

Clisby, H., Buckley, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

114

WS08.4 Feasibility of an incremental step test to assess aerobic fitness in adult cystic fibrosis

Beverley, Z., Parrott, H., Gray, C., Jones, A.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

115

WS08.5 Balance, flexibility and agility - additional aspects of physical fitness and trainability in children and adolescents with CF

Gruber, W., Tas, T., Blosch, C., Koerner-Rettberg, C., Dillenberger, S., Welsner, M., Sutharsan, S., Mellies, U., Stehling, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

116

WS10.3 CF newborn screening in Austria: after 20 years changing the algorithm from IRT/IRT to IRT/PAP/IRT

Renner, S., Schanzer, A., Metz, T., Szépfalusi, Z., Zeyda, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

117

WS10.5 The Irish Comparative Outcome Study (ICOS): clinical outcomes at 3 years following introduction of newborn cystic fibrosis screening

Fitzpatrick, P., Fitzgerald, C., Ni Chroinin, M., Mullane, D., Herzig, M., Greally, P., Healy, F., Mcnally, P., Javadpour, S., Cox, D., George, S., Linnane, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

118

WS10.6 Seven years of nationwide cystic fibrosis newborn screening in the Czech Republic: analysis of the IRT/DNA/IRT scheme outcomes

Holubová, A., Gaillyová, R., Skalická, V., Vinohradská, H., Dejmek, P., Libik, M., Valášková, I., Bartošová, J., Doušová, T., Holčíková, A., Homola, L., Kinclová, E., Votava, F., Macek, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

119

WS11.4 The repurposed multiple sclerosis drug, glatiramer acetate, is an antibiotic resistance breaker in Pseudomonas aeruginosa strains from cystic fibrosis patients

Murphy, R.A., Harrison, J., Tsikna, L., Davies, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

120

WS11.6 The effect of 2-thiopyridine derivative 11026103, a novel antibacterial compound, on Burkholderia cenocepacia: transcriptomic response and resistance mechanisms

Nunvar, J., Buroni, S., Makarov, V., Cardona, S., Drevinek, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

121

WS12.3 Telehealth monitoring for home intravenous antibiotics in cystic fibrosis

Blanch, L., Gurney, A., Watkins, R., Anderson, A., Echevarria, C., Doe, S., Bourke, S.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

122

WS12.4 Are goal-focused, motivational text messages effective at improving patients’ belief in their own ability (self-efficacy) to complete inhaled therapies in adults with cystic fibrosis

Channon, K., Reilly, C.C., Massey-Chase, R., Elston, C., Nikoletou, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

123

WS12.5 A smartphone application for reporting symptoms in adults with cystic fibrosis: a randomised controlled trial

Wood, J., Jenkins, S., Putrino, D., Mulrennan, S., Morey, S., Cecins, N., Bear, N., Hill, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

124

WS12.6 MyCyFAPP project: validation of the PEDsQL GI symptom scale to evaluate gastro-intestinal symptoms in children with cystic fibrosis

Boon, M., Claes, I., Havermans, T., Fornés-Ferrer, V., Asseiceira, I., Bulfamente, A., Garriga, M., Masip, E., Woodcock, S., Walet, S., Barreto, C., Calvo-Lerma, J., Colombo, C., Crespo, P., Van der W

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

125

WS13.1 Thoracic ultrasound as a useful tool to assess lung atelectasic areas and set the best physiotherapy

Giuliari, M., Vicentini, L., Tilotta, F., Paciaroni, A., Della Sala, S., Guerzoni, C., Polloni, C., Dinnella, G., Gallo, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

126

WS13.2 Musculoskeletal symptoms in adult with cystic fibrosis

Clarke, E.A., Taylor, J.C., Watson, P., Freeston, J.E., Hamid, A., Ho, P., Peach, C.A., Peckham, D., Jones, A.M., Horsley, A.R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 67 KB

english, 2018

127

WS13.4 Experiences of non-invasive ventilation in a large adult cystic fibrosis centre and nationally

Beverley, Z., Parrott, H., Jones, A.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

128

WS13.6 Urinary incontinence in adult patients with cystic fibrosis: prevalence, impact on daily life and relationship with chronic cough

Crisafulli, E., Faverzani, S., Scandolo, P., Longo, F., Chetta, A.A., Pisi, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

129

WS14.4 Use of computational fluid dynamics (CFD) to model aerosol deposition in the lungs of patients with cystic fibrosis

Hull, D., Black, A., Vos, W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

130

WS14.5 A randomised controlled pilot study of sildenafil to treat exercise intolerance in moderate to severe cystic fibrosis

Taylor-Cousar, J.L., Hunt, K.C., St. Clair, C., Everett, D.C., Nick, J.A., Saavedra, M.T., Abman, S.H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

131

WS15.1 From the bench to bedside: expanding CFTR modulators to rare mutations by response assessment in patients-derived materials and cellular models

Silva, I.A.L., Ramalho, S., Awatade, N.T., Centeio, R., Farinha, C.M., Amaral, M.D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

132

WS15.3 Patterns of response to lumacaftor and ivacaftor in rectal organoids

Ramalho, A.S., Peetermans, P., Proesmans, M., Dupont, L., Vermeulen, F., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

133

WS16.2 Serum levels of PAD4 auto-antibodies correlate with airway obstruction in cystic fibrosis patients: novel systemic marker of lung disease?

Yadav, R., Stecenko, A., Rada, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

134

WS16.3 Investigation of inflammatory and fibrotic biomarkers in the sputum of cystic fibrosis patients

Thomassen, J.C., Walz, M.-L., Trojan, T., Lippach, G., Rietschel, E., Alejandre Alcazar, M.A., van Koningsbruggen-Rietschel, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

135

WS16.5 Examining serum T H 2 inflammatory exacerbation biomarkers in CF

Siedlecki, A., Quon, B.S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

136

WS17.4 How organoid assay results concur with the clinical phenotype in an unusual patient with S1251N/G542X

Cuyx, S., Bosch, B., Vermeulen, F., Proesmans, M., Cuppens, H., Peetermans, P., Ramalho, A.S., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

137

WS17.6 Characteristics of the reproductive system in adult male patients with cystic fibrosis

Repina, S., Krasovsky, S., Rozhivanov, R., Bogoliubov, S., Sorokina, T., Andreeva, M., Shtaut, M., Kurilo, L., Shmarina, G., Adyan, T., Stepanova, A., Polyakov, A., Amelina, E., Kapranov, N., Kondrate

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

138

WS18.1 Waiting for lung transplant, manifold experiences: a literature review

Skogeland, U., de Monestrol, I., Godskesen, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

139

WS18.4 Evaluation of transplantation information delivered to patients and their relatives by the professionals from cystic fibrosis centres and transplant centres and from transplanted peer-patients in France

David, V., Perrin, A., Pougneon-Bertrand, D., Kanaan, R., Kerbrat, M., Le Rhun, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

140

WS19.1 Glucose abnormalities in Canadian and French cystic fibrosis patients: a Glyc-one database analysis

Reynaud, Q., Boudreau, V., Touzet, S., Desjardins, K., Poupon Bourdy, S., Berthiaume, Y., Rabasa Lhoret, R., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 72 KB

english, 2018

141

WS19.4 Glucose and insulin area under the curve (AUC) can differentiate between cystic fibrosis patients that may benefit from early insulin treatment

Soesman, L., Miari, S., Breuer, O., Bentur, L., Tsabari, R., Elyashar-Earon, H., Armoni, S., Gur, M., Teleshov, A., Sprikkelman, A., Zangen, D., Kerem, E., Cohen-Cymberknoh, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 67 KB

english, 2018

142

WS19.5 The main mechanism associated with glucose intolerance in older patients with cystic fibrosis is insulin resistance and not progressive insulin secretion deficit

Boudreau, V., Colomba, J., Lehoux Dubois, C., Desjardins, K., Rabasa-Lhoret, R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

143

WS19.6 Feasibility and efficacy of combined lung and pancreatic islet transplantation in Cystic Fibrosis-Related Diabetes: a pilot study

Wagner, C., Porzio, M., Olland, A., Reeb, J., Greget, M., Grenet, D., Bouilloud, F., Bonnette, P., Berney, T., Javelot Jacquelin, C., Baltzinger, P., Kessler, R., Kessler, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

144

EPS1.05 CAT-5571 restores autophagy, a fundamental defect in cystic fibrosis, and is a potential new treatment for people with cystic fibrosis

Liu, F., Krause, K., Amer, A., Hall-Stoodley, L., Reilly, J.F., Nichols, A.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 63 KB

english, 2018

145

EPS1.06 Overproduction of IL-6 and TNF through IRE1α is CFTR genotype dependent

Lara Reyna, S., Scambler, T., Holbrook, J., Wong, C., Jarosz-Griffiths, H., Martinon, F., Savic, S., Peckham, D., Mcdermott, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 63 KB

english, 2018

146

EPS2.04 Combination of liver cirrhosis with mild mutation p.E92K

Gorinova, Y., Krasovsky, S., Pyaterkina, O., Baykova, G., Cherniak, A., Simonova, O.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

147

EPS2.06 Phenotypic manifestations of rare missense mutations

Krasovsky, S., Gorinova, Y., Amelina, E., Polyakov, A., Petrova, N., Kondratyeva, E., Voronkova, A., Nikonova, V., Simonova, O., Stepanova, A., Adyan, T., Ivaschenko, T., Nasykhova, Y., Afanasyeva, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

148

EPS2.08 Clinical characteristics of patients with one known cystic fibrosis-related mutation despite extended genotype testing

Brockelsby, C., Frost, F., Griffiths, P., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 67 KB

english, 2018

149

EPS3.03 Effects of lumacaftor-ivacaftor therapy on CFTR function in Phe508del homozygous patients with cystic fibrosis

Graeber, S.Y., Dopfer, C., Naehrlich, L., Gyulumyan, L., Scheuermann, H., Hirtz, S., Wege, S., Mairbäurl, H., Dorda, M., Hyde, R., Bagheri-Hanson, A., Rueckes-Nilges, C., Fischer, S., Mall, M.A., Tümm

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

150

EPS3.04 Impact of CFTR modulation with ivacaftor on gut microbiota and intestinal inflammation

Ooi, C.Y., Syed, S.A., Rossi, L., Garg, M., Needham, B., Avolio, J., Young, K., Surette, M., Gonska, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

151

EPS3.06 Safety, pharmacokinetics and pharmacodynamics of the CFTR corrector FDL169

Horsley, A., Burr, L., Kotsimbos, T., Ledson, M., Schwarz, C., Simmonds, N., O'toole, T., Kolodziej, A.F., Ordonez, C.L., Bell, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

152

EPS4.04 Characterising the intestinal virome in cystic fibrosis

Coffey, M.J., Low, I., Stelzer-Braid, S., Rawlinson, W., Thomas, T., Jaffe, A., Ooi, C.Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

153

EPS4.08 NTM infection in paediatrics: how do we approach these emerging pathogens?

Saint, G.L., Thomas, M.F., Langley, R., Brodlie, M., Mcnamara, P.S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

154

EPS5.01 Personalised time-updated predictions of short-term and long-term survival in CF using UK Registry data

Keogh, R., Barrett, J., Seaman, S., Szczesniak, R., Taylor-Robinson, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

155

EPS5.02 Estimation of survival of cystic fibrosis patients in France by two different methods

L'hostis, C., Dehillotte, C., Lemonnier, L., Bellis, G., Rault, G., Ramel, S., Burgel, P.-R., Férec, C., Scotet, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

156

EPS5.04 The role of Pseudomonas infection in early growth trajectories in cystic fibrosis

Macdougall, A., Carr, S.B., Archangelidi, O., Keogh, R.H., Cullinan, P., Bilton, D., Jarvis, D., Stanojevic, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

157

EPS5.08 Quality improvement in CF: what can we learn from each other? A statistical analysis of UK Registry data and consultations with clinicians and patients

Macneill, S.J., Pierrotti, L., Mohammed, M.A., Wildman, M., Boote, J., Harrison, S., Carr, S.B., Cullinan, P., Elston, C., Bilton, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 67 KB

english, 2018

158

EPS6.03 Hypertonic saline use in our paediatric cystic fibrosis centre: using the UK cystic fibrosis Registry to reflect on practice

O'connor, R., Miller, J., Nwokoro, C., Pao, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

159

EPS6.06 Influence of a supervised exercise program ( CFmobil ) on motor ability in adult cystic fibrosis patients

Welsner, M., Sutharsan, S., Stehling, F., Tas, T., Thra, D., Koerner-Rettberg, C., Benzrath, S., Gruber, W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

160

IPD1.01 Mental health screening in cystic fibrosis centres across Europe

Abbott, J., Havermans, T., Jarvholm, S., Landau, E., Prins, Y., Popa, N., Smrekar, U., Staab, D., Verity, L., Verkleij, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 263 KB

english, 2018

161

IPD1.02 Assessing strengths and difficulties as part of annual mental health screening

Duff, A.J., Latchford, G.J., Fisher, C., Vuister, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 263 KB

english, 2018

162

IPD1.06 Outcome mental screening among Swedish adolescents with CF

Laine, C., Bergenmar Ivarsson, E., Larsson, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

163

IPD1.07 Cystic fibrosis: does the deterioration of pulmonary function affect the level of anxiety and depression?

Lalic, I., Vukić Dugac, A., Zovko, T., John, V., Tješić-Drinković, D., Samaržija, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

164

IPD2.03 The effects of 3-year ivacaftor use on lung function and intravenous days seen in UK CF Registry Data

Newsome, S.J., Keogh, R.H., Daniel, R.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

165

IPD2.04 Long-term effects of ivacaftor in patients with G551D mutation and mild lung disease

Ellemunter, H., Hindinger, C., Steinkamp, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

166

IPD2.05 Effects of ivacaftor in patients with cystic fibrosis and severe lung disease carrying CFTR mutations with residual function

Salvatore, D., Braggion, C., Messore, B., Pisi, G., Tuccio, G., Bena, C., Colangelo, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 76 KB

english, 2018

167

IPD2.06 Ivacaftor therapy in patients with severe baseline lung disease carrying a residual function mutation

Mitchell, R.M., Horsley, A.R., Jones, A.M., Barry, P.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

168

IPD2.09 Lumacaftor/ivacaftor improves 6 minute walk test distance, FEV 1 and reduces exacerbations in severe cystic fibrosis lung disease

Thiruchelvam, T., Cookson, K., Wark, P., Dorahy, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

169

IPD2.11 The potentially beneficial CNS-activity profile of ivacaftor and its metabolites

Schneider, E., Carbone, V., Wilson, J., Button, B., Hoyer, D., Li, J., Velkov, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

170

P004 Results of a 3-year screening in Konya province and the frequency in our region

Pekcan, S., Büyükkaya, Z., Şahlar, T.E., Karakaş, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

171

P007 Current situation of genotyping of cystic fibrosis patients in the Russian Federation

Kashirskaya, N.Y., Amelina, E.L., Krasovskiy, S.A., Kondratyeva, E.I., Voronkova, A.Y., Chernyak, A.V., Gembitskaya, T.E., Svetlichnaya, I.G., Bulatova, I.A., Tryastsyna, N.V., Tutueva, L.A., Ivakhnen

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

172

P009 Fast detection of CFTR mutations in dried blood spots of newborns in Khanty-Mansi region (Russia)

Donnikov, M.Y., Meshcheryakov, V.V., Kolbasin, L.N.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

173

P012 Comparison of 2 strategies of newborn screening (NBS) for cystic fibrosis (CF): IRT/IRT vs. IRT/PAP

Teper, A., Smithuis, F., Rodriguez, V., Salvaggio, O., Macallini, G., Micenmacher, V., Aranda, C., García-Bournissen, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

174

P014 Genetic study of patients with CF in a mixed population of northeastern Brazil

Mota, L.R., de Castro, L.L., de Melo Filho, V.M., dos Santos, J.F., de Lima, R.L.L.F., Toralles, M.B.P., Souza, E.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 76 KB

english, 2018

175

P015 First molecular report of the ΔF508 mutation in patients with cystic fibrosis in Paraguay

Ascurra, M., Espínola Monges, D., Vega Gomez, C., Ortiz Paranza, L., Valenzuela, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

176

P017 A comparative study between clinically diagnosed and screen-detected children with cystic fibrosis: parents’ economic costs prior to diagnosis

Fitzpatrick, P., Fitzgerald, C., Ceilleachair, A.Ó., Kapur, K., Staines, A., Linnane, B., George, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 62 KB

english, 2018

177

P021 A phase 3, open-label study of tezacaftor/ivacaftor (TEZ/IVA) therapy: interim analysis of pooled safety, and efficacy in patients homozygous for F508del-CFTR

Flume, P., Lekstrom-Himes, J., Fischer Biner, R., Simard, C., Downey, D.G., Zhou, H., Owen, C.A., De Boeck, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

178

P022 Safety, tolerability and pharmacokinetics of CFTR corrector FDL169

Ordonez, C.L., Horsley, A., Chai, J., Kolodziej, A.F., Elborn, S., Ferkany, J.W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

179

P023 Impact of lumacaftor/ivacaftor (Orkambi ® ) on proton pump inhibitor use in adult cystic fibrosis patients

Connolly, A., Moran, M., Keane, C., Mckone, E., Gallagher, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

180

P026 Real-world Orkambi Cohort Cork study (ROCKS) - a prospective three months’ analysis addressing the impact of CFTR modulation in patients with cystic fibrosis homozygous for ΔF508del CFTR

Arooj, P., Ronan, N., Mccarthy, Y., Daly, M., Flanagan, E., Shortt, C., Mccarthy, M., Flemming, C., Eustace, J.A., Murphy, D., Plant, B.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

181

P029 Upper airway symptoms in CF - is dornase alfa administered by pulsating aerosol a treatment option?

Haynes, F., Ledermueller, R., Mentzel, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

182

P032 The analgesic effect of salmon calcitonin on acute rib fractures in cystic fibrosis

Lee, A.C., Ewence, A.E., Bowman, E., Jones, A.L., Shah, A., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

183

P034 Are patients with cystic fibrosis in clinical trials sensitive to the placebo effect? A metanalysis

Coton, J., Le, H.-H., Veuillet, V., Janiaud, P., Cucherat, M., Kassai-Koupai, B., Gueyffier, F., Reix, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

184

P037 In vivo confirmation of Pseudomonas aeruginosa biofilms as independent pharmacological compartments - implication for antibiotic treatment

Christophersen, L., Cao, B., Lerche, C., Thomsen, K., Høiby, N., Moser, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

185

P038 Intraclonal competitive fitness of serial Pseudomonas aeruginosa isolates from cystic fibrosis lungs

Cramer, N., Fischer, S., Hedtfeld, S., Dorda, M., Klockgether, J., Wiehlmann, L., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

186

P039 Monitoring of chronic Pseudomonas aeruginosa lung infection in cystic fibrosis patients

Avetisyan, L., Chernukha, M., Siyanova, E., Shaginyan, I., Prilipov, A., Kondratyeva, E., Kashirskaya, N., Zhekayte, E., Krasovsky, S., Usacheva, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

187

P040 Carbapenem-resistant shared Pseudomonas aeruginosa strains with oprD mutations in cystic fibrosis

Sherrard, L., Duplancic, C., Wee, B., Ramsay, K., Webster, S., Kidd, T., Whiley, D., Beatson, S., Bell, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

188

P041 Multi-drug resistant Pseudomonas aeruginosa strains in cystic fibrosis and FEV 1 decline

Dolce, D., Ravenni, N., Campana, S., Braggion, C., Taccetti, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 74 KB

english, 2018

189

P043 Antimicrobial resistance of CF Pseudomonas aeruginosa : a longitudinal study from initial colonisation in CF patients with special focus on temocillin

Dupont, C., Daniel, T., Martocq, N., Benaoudia, M., Pantel, A., Jumas-Bilak, E., Chiron, R., Marchandin, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

190

P045 Strain and antibiogram changes, over time, in paediatric cystic fibrosis patients colonised with Pseudomonas aeruginosa

Mushtaq, S., Vickers, A., Payne, Z., Kenna, D., Turton, J.F., Woodford, N., Livermore, D.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

191

P047 Detection of Pseudomonas aeruginosa in exhaled breath of cystic fibrosis patients

Neerincx, A.H., Brinkman, P., van der Gouwe, P., Pfaff, T., Fens, N., Gerritsen, M., Haarman, E., van Aalderen, W.M.C., Majoor, C.J., Weersink, E.J.M., Bos, L.D., Sterk, P.J., Maitland-van der Zee, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

192

P049 Phenotyping and molecular typing of Achromobacter spp. strains in children and adults with cystic fibrosis in the Russian Federation

Chernukha, M., Kulyastova, D., Avetisyan, L., Shaginyan, I., Zhuhovitsky, V., Kondratyeva, E., Grumov, D., Soloviev, A., Polyakov, N., Voronkova, A., Sherman, V., Kapranov, N., Amelina, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

193

P050 Chronic infection with Achromobacter xylosoxidans in paediatrics and adults cystic fibrosis patients in two centres from Argentina

Baran, E., Gil, F., Bettiol, M., Palau, M.J., D'alessandro, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

194

P051 Contribution of Stenotrophomonas maltophilia in colonisation of the respiratory tract in CF patients

Semczuk, K., Wojcieszek, A., Dmeńska, H., Fronc, B., Romanowska, E., Dzierżanowska-Fangrat, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

195

P052 Late impact of early chronic methicillin-sensitive Staphylococcus aureus (MSSA) infection in children with cystic fibrosis

Galode, F., Fayon, M., Bui, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

196

P053 Use of extended-quantitative culture does not predict an imminent pulmonary exacerbation

Sherrard, L., Einarsson, G., Johnston, E., O'neill, K., Mcilreavey, L., Mcgrath, S., Gilpin, D., Murray, M., Lavelle, G., Mcelvaney, G., Boucher, R., Muchlebach, M., Elborn, J.S., Tunney, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

197

P055 A cross-sectional analysis of cough swabs from non-expectorating CF patients and healthy control participants

Einarsson, G.G., Sherrard, L.J., Johnston, E., O'neill, K., Mcllreavey, L., McGrath, S.J., Gilpin, D.F., Murray, M., Lavelle, G., McElvaney, G., Muhlebach, M., Elborn, J.S., Tunney, M.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 75 KB

english, 2018

198

P057 Brain abscess caused by Escherichia coli in an adult with cystic fibrosis

Baran, E., D’ Ascenzo, V., Volta, L., Granero, N., Hendriksen, B., Menna, L., Zattera, E., Gastal, S., Negroni, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

199

P058 Prevalence of shared Mycobacterium abscessus complex (MABSC) in the Queensland cystic fibrosis population

Stockwell, R.E., Leong, L.E.X., Wheeler, N.E., Bryant, J.M., Wood, M.E., Sherrard, L.J., Thomson, R.M., Rogers, G., Wainwright, C.E., Parkhill, J., Floto, R.A., Bell, S.C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

200

P059 Epidemiology of nontuberculous mycobacteria at an adult cystic fibrosis centre

Greener, T., Frost, F., Walshaw, M., Wat, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 76 KB

english, 2018

201

P060 The epidemiology of nontuberculous mycobacteria in a paediatric cystic fibrosis centre

Kotnik Pirš, A., Žolnir Dovč, M., Krivec, U., Aldeco, M., Lepej, D., Zver, A., Praprotnik, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

202

P061 The use of aprepitant as part of an effective anti-emetic regimen to facilitate successful completion of intensive intravenous (IV) Mycobacterium abscessus therapy

Belkarty, B.B., Jamali, A., Harrison, M., Ross, J., Shah, A., Jones, A.L., Elborn, J.S., Simmonds, N.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

203

P067 Diverse clinical characteristics of Aspergillus growth in patients with cystic fibrosis

Emiralioglu, N., Dogru, D., Dogan, O., Gulmez, D., Arikan-Akdagli, S., Eryilmaz, S., Tugcu, G., Gharibzadeh Hizal, M., Yalcin, E., Ozcelik, U., Sener, B., Kiper, N.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

204

P068 Presence of Candida dubliniensis in the cystic fibrosis respiratory tract was associated with a significant decline in lung function – results from a 16-year retrospective study

Al Shakirchi, M., Klingspor, L., Bergman, P., de Monestrol, I., Hjelte, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

205

P074 Information value of non-invasive specimens for airway bacteriome research

Voronina, O., Ryzhova, N., Kunda, M., Aksenova, E., Sharapova, N., Sherman, V., Voronkova, A., Kondratyeva, E., Gintsburg, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

206

P075 Anti-fungal therapeutic drug monitoring in adults with cystic fibrosis

Dave, K., Di Paolo, M., Vijayasingam, A., Sheth, R., Luke, E., Scourfield, A., Nwankwo, L., Schelenz, S., Elborn, J.S., Armstrong-James, D., Shah, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

207

P076 What should you do after stopping flucloxacillin in children?

Azzopardi, K., Hall, S., Forton, J., Thia, L., Doull, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

208

P079 The impact of non-antimicrobial therapies on bacterial pathogens commonly found in cystic fibrosis airways

Kirkwood, Z.I., Millar, B.C., Moore, J.E., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

209

P080 Potential taste disturbance is largely mild and diminishes with continuing treatment in cystic fibrosis patients treated with levofloxacin inhaled solution

Schwarz, C., Spinola, M., Flume, P.A., Elborn, J.S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

210

P083 Inhaled anti-pseudomonal therapy in patients with cystic fibrosis

Hector, A., Leinert, J., Eickmeier, O., Neuner, D., Griese, M., Eber, E., Kirn, T., Hartl, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 72 KB

english, 2018

211

P086 Characterisation of colistimethate sodium delivery from different nebuliser systems

Hull, D., Black, A., Degtyareva, Y., Hatley, R.H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

212

P087 Monitoring amikacin pharmacokinetics for personal dose optimisation

Leshem, R., Gileles-Hillel, A., Cohen-Cymberknoh, M., Tsabari, R., Kerem, E., Shoseyov, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

213

P093 Oral versus intravenous treatment of bronchopulmonary exacerbations in cystic fibrosis

Wimmer, E., Holz, F., Eschenhagen, P., Brandt, C., Barthel, N., Kaufmann, S., Röhmel, J.F., Staab, D., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

214

P094 Design, enrollment, and feasibility of the STOP-2 randomised study of intravenous antibiotic treatment duration in cystic fibrosis pulmonary exacerbations

Flume, P.A., Heltshe, S.L., West, N.E., Vandevanter, D.R., Sanders, D.B., Skalland, M., Beckett, V., Goss, C.H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

215

P096 Influenza vaccination in children with cystic fibrosis using live attenuated influenza vaccine: experience from five seasons in an Austrian children CF centre

Renner, S., Gruber, S., Nachbaur, E., Bannert, C., Gona-Hoepler, M., Szépfalusi, Z.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

216

P099 Pneumococcal antibody levels in cystic fibrosis patients attending the All Wales Adult CF Centre

Speight, L., Smith, A., Thomas, L., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

217

P102 First Aspergillus fumigatus seroconversion was associated with more severe disease in cystic fibrosis children

Petat, H., Couderc, L., Favennec, L., Marguet, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

218

P106 Outcome of adults with cystic fibrosis admitted to the medical intensive care unit

Er, B., Ortaç Ersoy, E., Öcal, S., Topeli İskit, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

219

P107 Heart rate as predictor of cystic fibrosis severity

Ferro, F., Ruivo, P., Rodrigues, T., Lopes, C., Azevedo, P., Bárbara, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 79 KB

english, 2018

220

P108 Cell-free DNA and DNase I activity in cystic fibrosis

Kondratyeva, E.I., Kostyuk, S., Ershova, E., Voronkova, A., Sherman, V., Zhekayte, E., Melyanovskaya, Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 65 KB

english, 2018

221

P109 In vitro effects of rhDNase on sputum in patients with cystic fibrosis using rheology

Ghiringhelli, E., Patarin, J., Perceval, M., Mazur, S., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 65 KB

english, 2018

222

P110 In vivo effects of rhDNase and saline solution on sputum in patients with cystic fibrosis using rheology

Patarin, J., Ghiringhelli, E., Cracowski, C., Camara, B., Quétant, S., Bosc, C., Pison, C., Cracowski, J.-L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 65 KB

english, 2018

223

P111 Testing sputum in patients with cystic fibrosis using rheology: the ageing effect

Patarin, J., Ghiringhelli, E., Camara, B., Benitez, J.-C., Quétant, S., Pison, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 83 KB

english, 2018

224

P112 Exhaled nitric oxide is a possible biomarker for predicting complications in cystic fibrosis patients

Renner, A., Kaluza, I., Marth, K., Moeslinger, T., Pohl, W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

225

P118 Differences in molecular diffusivity do not explain discrepancy in Lung Clearance Index measured by nitrogen and SF6 washout

Whitfield, C.A., Jensen, O.E., Horsley, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

226

P122 Change in the Lung Clearance Index (LCI) with microbiological status in children with cystic fibrosis - pilot study in a new paediatric cystic fibrosis centre in Poland

Walicka-Serzysko, K., Postek, M., Sands, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 75 KB

english, 2018

227

P127 The role of the specialist cystic fibrosis pharmacist in embedding adherence monitoring of inhaled therapies into clinical care

Mckeown, C., Caskey, S., Downey, D.G., Rendall, J., Addy, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

228

P130 Immunosuppression in cystic fibrosis: how worried should we be?

Clarke, E.A., Ibrahim, M., Martin, K., Freeston, J.E., Watson, P., Peckham, D., Jones, A.M., Horsley, A.R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 64 KB

english, 2018

229

P131 Persistence of peribronchial tertiary lymphoid structures in cystic fibrosis patients treated with rituximab

Regard, L., Martin, C., Zemoura, L., Geolier, V., Sage, E., Burgel, P.-R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

230

P134 Teaching adult patients CF physiotherapy: a French experience

Lejosne-Artige, C., Gauchez, H., Perrot-Minnot, C., Christoflour, N., Giovannetti, P., Borel, B., Tayabaly, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

231

P137 Retrospective clinical data on IPV therapy in children with cystic fibrosis

Anderson, P., Johnstone, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

232

P140 The minimal clinically important difference for survival in patients with cystic fibrosis

Doeleman, W.R., Hulzebos, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

233

P144 Exercise: love it, hate it, or somewhere in-between? Identifying exercise self-efficacy and the impact of personal training in children and young people with CF

Douglas, H., Bryon, M., Denford, S., Rand, S., Main, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

234

P145 Development of Hacka Health 4 CF: a physiotherapy technology solution to support young people with cystic fibrosis

Rand, S., Prasad, S.A., Balmer, G., Kent, J., Copeland, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

235

P146 Impact of the optimal duration of intensive rehabilitation training on patients with moderate to severe cystic fibrosis

Gauchez, H., Chaabi, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

236

P147 Virtual exercise class for CF in patients – a novel way to encourage exercise participation

Haynes, F., Cook, M., Mosley, K., Millward, S., Dewar, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

237

P151 Feasibility of following up the benefits of a rehabilitation program by telehomecare in children with cystic fibrosis

Bruneaux, C., Bouteleux, B., Guesnier, J., Lacour, A., Galodé, F., Bui, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

238

P156 Mobile phone step-counter data does not correlate with objective measures of exercise capacity

Griffiths, P., Calvert, P., Hilton, N., Frost, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

239

P158 Patient-friendly glucose tolerance test for patients with cystic fibrosis

Amstelveen-Bokkerink, S., Erren, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

240

P163 Cystic Fibrosis-Related Diabetes, chronic lung infection and low nutritional status increase the risk of cystic fibrosis related bone disease

Kotnik Pirš, A., Šmigoc Schweiger, D., Praprotnik, M., Aldeco, M., Zver, A., Battelino, T., Oštir, M., Korenin, K., Krivec, U.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

241

P165 Hyperglycemia may predispose to lower respiratory tract infection in young children with cystic fibrosis

Prentice, B., Hameed, S., Verge, C.F., Ooi, C.Y., Strahan, R., Waters, S., Widger, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

242

P166 The use of dipeptidyl peptiddase-4 (DPP-4) inhibitors in cystic fibrosis

Farrell, E., Watson, K., Hutchings, P., Noble-Bell, G., Macedo, P., Elston, C., Hopkins, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

243

P167 Understanding the mechanisms for the increased prevalence of gastro-oesophageal reflux in cystic fibrosis

Lord, R.W., Casey, J., Houghton, L.A., Treadway, S., Jones, R., Barry, P.J., Whorwell, P.J., Smith, J.A., Jones, A.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

244

P168 The relationship between gastro-oesophageal reflux and CF lung disease

Lord, R.W., Treadway, S., Bianco, B., Jones, R., Barry, P.J., Mcnamara, P.S., Whorwell, P.J., Smith, J.A., Jones, A.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

245

P171 How to give pancreatic enzyme in cystic fibrosis children with gastrostomy and unable to swallow opotherapy by mouth?

Collard, C., Delacollette, F., Boboli, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

246

P175 Cystic fibrosis-related fatty liver disease is associated with Pseudomonas aeruginosa infection and reduced lung function

Wrey, C., Schmidt, A., Fitzpatrick, E., Abusamra, R., Gupta, A., Ruiz, G., Pianosi, P., Bossley, C.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

247

P176 Features of clinical status in children with cystic fibrosis complicated by liver cirrhosis and portal hypertension in the Russian Federation

Voronkova, A., Kondratyeva, E., Tsirulnikova, O., Malomuzh, O., Ilyenkova, N., Kashirskaya, N., Sherman, V., Chernyak, A., Smirnova, V., Stezhkina, E., Budzynskiy, R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

248

P177 Is APRI index evaluation useful in diagnosing hepatic changes in the course of cystic fibrosis?

Wiecek, S., Wos, H., Pogorzelski, A., Kordys-Darmolinska, B., Mazurek, H., Grzybowska-Chlebowczyk, U.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

249

P178 Sodium status in children with CF: evaluation of fractional sodium excretion in a paediatric cohort

Proesmans, M., Dings, A., Van Meerbeek, S., Boon, M., De Boeck, K., Vermeulen, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

250

P179 A retrospective audit of sodium chloride supplementation in infants with cystic fibrosis

Stead, K., Desai, M., Patchell, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

251

P180 Salt supplementation in CF: too much or too low?

Chakraborty, S., Nwokoro, C., Mclean, M., Pao, C.S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

252

P182 An analysis of vitamin K supplementation during the first five years of life in paediatric cystic fibrosis patients managed at Addenbrooke's hospital, Cambridge

Kelly, S., Polychronakis, T., Selby, L., Thoppil, V., Middleton, C., Lee, J., Mcshane, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

253

P183 Identification of subclinical deficit of vitamin K in cystic fibrosis by Micro-Raman spectroscopy

Silva, A.R., Batista de Carvalho, A., Almeida, S., Maia, C., Ferreira, R., Marques, M.P., Batista de Carvalho, L., Roda, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

254

P185 The feasibility and applicability of the Healthy Eating Index for Australian Adults (HEIFA-2013) score for dietary assessment in adults with cystic fibrosis

King, S.J., Thompson, S., Taylor, G., Malesic, L., George, E.S., Tierney, A.C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

255

P187 Evolution of body composition measured by BIA after the start of tube feeding

Van Biervliet, S., De Baets, F., Van Braeckel, E., Van daele, S., Van Meerhaeghe, S., Declercq, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

256

P188 Bio-electrical impedance analysis and relationship with pulmonary function in cystic fibrosis patients

Hollander, F.M., Roelofs, J., van der Boom, S.T., Burghard, M., de Roos, N.M., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

257

P189 Body composition measured by BIA of tube-fed cystic fibrosis patients compared to age-sex matched CF controls

Van Biervliet, S., Van Braeckel, E., De Baets, F., Van daele, S., Van Meerhaeghe, S., Declercq, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

258

P191 Gender differences in lipid profiles in adults with cystic fibrosis

Caskey, S., Lynch, V., Addy, C., Mccaughan, J., Rendall, J.C., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

259

P198 Evaluation of the effect of dietary therapy after PEG insertion on anthropometric and respiratory indices in patients with cystic fibrosis

Jazgarska, P., Mazurek, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

260

P199 Nutritional status and eating behaviour in a CF population

Martins, T., Vaz, A.R., Asseiceira, I., Mexia, S., Pereira, L., Lopes, C., Almeida Nunes, P., Azevedo, P., Barreto, C., Sampaio, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

261

P200 Food diary analysis and growth: do they correlate? A pilot study

Smith, C., Chetty, K., Kapur, A., Seddon, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

262

P205 Influences on vitamin D in cystic fibrosis patients

Dediu, M., Ciuca, I.M., Pop, L.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

263

P210 Inflammation and bone turnover markers in cystic fibrosis

Mathiesen, I.H., Katzenstein, T.L., Mikkelsen, C.R., Pressler, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 65 KB

english, 2018

264

Hypoglycaemia in patients with cystic fibrosis- harbinger of poor outcomes or innocent bystander?

Moheet, Amir, Ode, Katie Larson

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 147 KB

english, 2018

265

Editorial Board

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

266

Editorial Board

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

267

P214 Vascular function in adults with cystic fibrosis

Shelley, J., Boddy, L.M., Knowles, Z.R., Stewart, C.E., Frost, F., Nazareth, D., Walshaw, M.J., Dawson, E.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

268

P216 Fertility in women with cystic fibrosis: a French survey

Tournier, A., Murris, M., Pienkowski, C., Bettiol, C., Guyard-Boileau, B., Parinaud, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

269

P218 Partnering with patients and parents of children with CF in the French care quality improvement program

Bertrand, D., Rault, G., David, V., Lombrail, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

270

P219 What do parents want from annual review?

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 63 KB

english, 2018

271

P222 Home delivery influences medicines possession ratio in adult cystic fibrosis

Dooney, M.K., Martin, K.J., Iqbal, N., Jones, A.M., Barry, P.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

272

P223 Totally implantable venous access device tip position and risk of venous complications in cystic fibrosis

Hart, A.O., Webb, K.M., Flight, W.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

273

P226 My day … my week: a new therapeutic educational tool in Liège Cystic Fibrosis Centre

Wuidart, M.-A., Natalini, N., Bodson, S., Hoquez, V., Boboli, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

274

P228 Genetic counselling: do our patients know what we think they know?

Wilson, C., Speight, L., Lau, D., Ketchell, R., Duckers, J., Edwards, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

275

P231 Adolescents with cystic fibrosis and the risk of acquiring and transmitting respiratory germs

Gonsseaume, S., Teixeira, M., Gérardin, M., Azaiz, W., Pesle, A., Munck, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

276

P242 Factors associated with medication adherence in adult cystic fibrosis patients

Uslu, N.Z., Olgun Yildizeli, S., Kocakaya, D., Ceyhan, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

277

P244 Fertility and fatherhood in men with cystic fibrosis (CF)

Anderson, A., Briggs, J., Doe, S., Echevarria, C., Stewart, J., Bourke, S.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

278

P245 Quality of life in cystic fibrosis: influence of some psychosocial factors on disease severity

Zorcec, T., Fustic, S., Jakovska, T., Spirevska, L., Stamatova, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

279

P246 Qualityof life and influencing factors in children and young adults with cystic fibrosis

Atag, E., Bas Ikizoglu, N., Ergenekon, P., Erdem Eralp, E., Gokdemir, Y., Karadag, B.T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

280

P247 Anxiety and depression in adult patients with cystic fibrosis in Croatia: results from an adult CF centre

Lalic, I., Vukić Dugac, A., Zovko, T., John, V., Tješić-Drinković, D., Tješić-Drinković, D., Samaržija, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

281

P248 Factors related to anxiety and depression in adult cystic fibrosis patients

Uslu, N.Z., Kocakaya, D., Olgun Yildizeli, S., Ceyhan, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

282

P250 Outcome measures as suggested by the CF community

Pavlou, H.E., Rowbotham, N.J., Leighton, P.A., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 49 KB

english, 2018

283

P251 How does the current clinical trials landscape reflect the James Lind Alliance top ten research priorities for CF?

Kalaitzis, I.S., Rowbotham, N.J., Smith, S.J., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

284

P253 Living with cystic fibrosis - are we all forgetting something?

Speight, L., Mcculloch, A., Byrne, A., Bayer, A., Sayers, A., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

285

P255 Demographic and clinical data of Croatian patients with cystic fibrosis – first results from the adult care CF centre

Markelić, I., Tješić Drinković, D., Tješić Drinković, D., Samaržija, M., Vukić Dugac, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

286

P256 Clinical and genetic characteristics of patients in a Lisbon CF Centre - importance in the face of CFTR targeted therapies

Rodrigues, T.P., Azevedo, P., Pereira, L.F., Celeste, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

287

P257 Characteristics of cystic fibrosis in regions of the Russian Federation

Kondratyeva, E., Krasovskiy, S., Cherniak, A., Voronkova, A., Sherman, V., Brisin, V., Khachiyan, M., Lyagusha, D., Ilyenkova, N., Chikunov, V., Melyanovskaya, Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

288

P262 The characteristics of chronic respiratory infection by Pseudomonas aeruginosa in the Register of the Patients with CF in the Russian Federation in 2016

Kondratyeva, E., Chernyak, A., Krasovskiy, S., Gembitskaya, T., Voronkova, A., Sherman, V., Amelina, E., Budzynskiy, R., Zhekayte, E., Kashirskaya, N., Osipova, E., Starodubtseva, O., Simanova, T., Ku

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 75 KB

english, 2018

289

P263 The health status of children with cystic fibrosis in Macedonia according to the CF Registry in 2015

Jakovska-Maretti, T., Fustik, S., Spireska, L., Zorcec, T., Stamatova, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

290

P265 Incidence of cystic fibrosis in Paraguay

Ascurra, M., Valenzuela, A., Salinas, M., Rodríguez, S., Porzio, G., Ortíz Paranza, L., Nuñez, A., Alvarez, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

291

P268 Pulmonary function patterns and their association with genotype and phenotype in adult cystic fibrosis patients

Stylemans, D., Verbanck, S., Vincken, S., Vincken, W., Vanderhelst, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

292

P269 Cystic Fibrosis-Related Diabetes (CFRD) before lung transplantation impact on survival and long-term renal function

Jardel, S., Touzet, S., Philit, F., Poupon Bourdy, S., Nove Josserand, R., Durupt, S., Durieu, I., Reynaud, Q.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

293

P270 Aminoglycoside exposure and renal function before lung transplantation in adult cystic fibrosis patients

Novel Catin, E., Pelletier, S., Reynaud, Q., Nove Josserand, R., Durupt, S., Dubourg, L., Fouque, D., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

294

P271 Malignant diseases in patients treated at the CF Centre Innsbruck

Appelt, D., Fuchs, T., Eder, J., Steinkamp, G., Ellemunter, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

295

P273 Human papilloma virus vaccination among female patients attending the Auvergne-Rhône Alpes paediatric cystic fibrosis centres

Rousset-Jablonski, C., Reix, P., Pin, I., Reynaud, Q., Llerena, C., Perceval, M., Touzet, S., Labbé, A., Durieu, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 69 KB

english, 2018

296

P276 Quality improvement in Registry data entry: experience from a UK centre

Pinnock, N., Aldous, G., Frost, F., Walshaw, M., Nazareth, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

297

Editorial Board

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 88 KB

english, 2018

298

WS02.4 Glycopeptidolipids of the Mycobacterium abscessus cell wall are immunodominant antigens and represent potential targets for a diagnostic assay

Schwarz, C., Lewin, A., Schäfer, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

299

WS02.6 Improving antibiotic activity against Mycobacterium abscessus isolates by inducing bacterial disaggregation and oxygen availability

Kolpen, M., Ravnholt, C., Qvist, T., Kragh, K.N., Fritz, B.G., Johansen, U.R., Bjarnsholt, T., Jensen, P.Ø., Høiby, N.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

300

WS03.5 The human intestinal proteome in children with cystic fibrosis

Coffey, M.J., Zhong, L., Jaffe, A., Ooi, C.Y., Waters, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 74 KB

english, 2018

301

WS05.1 Impact of newborn screening on outcomes and social inequalities in cystic fibrosis: a UK Registry-based study

Schlüter, D.K., Dryden, C., Southern, K.W., Diggle, P.J., Taylor-Robinson, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

302

WS07.2 Emergent biopsychosocial challenges of novel drug development and clinical trial participation: stopping an experimental modulator drug in order to conceive

Dobra, R., Simmonds, N., Weldon, P., Davies, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

303

WS07.3 The lonely patient: “I survived, now what?”

Landau, E.C., Mussaffi, H., Prais, D., Gendler, Y., Kadosh, D., Serfaty, D., Mantin, H., Mei-Zahav, M., Blau, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

304

WS07.5 Raising the medication intake in a kindergarten setting - a case report

Gabele, A., Möller, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

305

WS08.6 Effects of home-based adapted physical activity in patients with cystic fibrosis: an interventional study

Camara, B., Fuchs, A., Benitez, J.-C., Quetant, S., Chanoine, S., Llerena, C., Herbinet, A., Wuyam, B., Vion, V., Pin, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

306

WS10.2 International approaches for delivery of positive newborn bloodspot screening results for cystic fibrosis

Chudleigh, J., Ren, C.L., Barben, J., Southern, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

307

WS11.2 Hyperbaric oxygen treatment enhances the effect of tobramycin against biofilm-growing Pseudomonas aeruginosa

Møller, S.A., Ciofu, O., Jensen, P.Ø., Høiby, N., Kolpen, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

308

WS14.1 ROSCO-CF, a safety and efficacy clinical trial of (R)-roscovitine in cystic fibrosis patients

Meijer, L., Hery-Arnaud, G., Le Berre, R., Nowak, E., Rault, G., Mottier, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

309

WS14.3 Randomised, double-blind, controlled pilot study on safety and efficacy of hypertonic saline as preventive inhalation therapy in infants with CF (PRESIS)

Stahl, M., Ricklefs, I., Dopfer, C., Barth, S., Schlegtendal, A., Graeber, S.Y., Sommerburg, O., Diekmann, G., Wielpuetz, M.O., Kauczor, H.-U., Hüsing, J., Koerner-Rettberg, C., Naehrlich, L., Tümmler

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

310

WS15.5 Biomarkers to predict Orkambi efficacy: results of a prospective paediatric study

Masson, A., Hatton, A., Schneider, E., Berteloot, L., Lebourgeois, M., Chedevergne, F., Bailly, C., Kyrilli, S., Achimastos, D., Girodon, E., Edelman, A., Golec, A., Pranke, I., Sermet-Gaudelus, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

311

WS16.1 Early multi-dimensional assessment of Parameters to assess Response to Intra-Venous Antibiotic Treatment for pulmonary Exacerbations: The PRIVATE Study

Addy, C., Bradley, J., Bradbury, I., Elborn, J., Downey, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

312

WS16.4 Plasma YKL-40 levels and chitotriosidase activity in cystic fibrosis patients

Bal Topcu, D., Tugcu, G.D., Er, B., Esref, S., Hizal, M., Yalcin, E.E., Dogru Ersoz, D., Coplu, L., Ozcelik, U., Kiper, N., Lay, I., Oztas, Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

313

WS17.1 The multi-faceted nature of CFTR exonic mutations: impact on their functional classification

Bergougnoux, A., Bareil, C., Thèze, C., Sasorith, S., Audrézet, M.-P., Férec, C., Bienvenu, T., Girodon, E., Heller, M., Fanen, P., Mekki, C., Bieth, E., Fergelot, P., Gaston, V., Reboul, M.-P., Winte

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

314

WS17.2 Using a highly parallel sequencing assay for CFTR genotyping in ethnically diverse European patients with CF

Cuyx, S., Aertgeerts, E., Vermeulen, F., De Boeck, K., Cuppens, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

315

WS18.3 The introduction of a cystic fibrosis-specific advance care planning document

Cathcart, F., Beverley, Z., Tobin, T., Parrott, H., Madge, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

316

WS18.5 Does lung transplantation have an effect on the improvement of psychological status in patients with adult cystic fibrosis?

Lalic, I., Vukić Dugac, A., Zovko, T., John, V., Tješić-Drinković, D., Tješić-Drinković, D., Samaržija, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

317

WS19.3 Early screening and treatment of paediatric CF-Related Diabetes (CFRD) slows respiratory decline

Walker, C., Williams, S., McLean, M., Lambert, C., Pao, C., Nwokoro, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

318

EPS1.01 Chronic rhinosinusitis: reduced Ca 2+ -mediated Cl – secretion observed in vitro is confirmed by nasal potential difference measurements in patients

Salomon, J.J., Albrecht, T., Scheuermann, H., Gräber, S.Y., Baumann, I., Mall, M.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 270 KB

english, 2018

319

EPS3.02 Exploratory immune assays distinguish healthy volunteer from CF patient cohorts and were validated in a dose escalation study of QR-010 in subjects with cystic fibrosis homozygous for the F508del CFTR mutation

Noel, S., Leal, T., Obieglo, K., Nijholt, D., Lamontagne, N., Montgomery, S., Bujny, M.V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

320

EPS3.07 Safety, tolerability and pharmacokinetics of the CFTR potentiator FDL176

Ordonez, C.L., Chai, J., Kolodziej, A.F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 74 KB

english, 2018

321

EPS4.01 Microbial community composition in explanted cystic fibrosis lungs

Spence, C.D., Verleden, S., Einarsson, G.G., Mcdonough, J., Lee, A.J., Vos, R., Johnston, E., Janssens, W., Elborn, J.S., Verleden, G.M., Gilpin, D.F., Dupont, L., Vanaudenaerde, B., Tunney, M.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

322

EPS4.06 Mutual antagonism: a complex coexistence of Aspergillus fumigatus and Pseudomonas aeruginosa in the cystic fibrosis airway

Reece, E., Doyle, S., Renwick, J., Greally, P., Mc Clean, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

323

EPS5.07 Evaluating the impact of 2006 clinical practice guidelines for nutrition in children with cystic fibrosis in Australia

Ruseckaite, R., Pekin, N., King, S., Carr, E., Ahern, S., Oldroyd, J., Earnest, A., Sims, G., Wainwright, C., Armstrong, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

324

EPS6.04 Correlation between six-minutes-walk-test and cystic fibrosis disease severity

Ben-Meir, E., Eisenstadt, I., Israeli, T., Tsabari, R., Breuer, O., Reiter, J., Gileles-Hillel, A., Shoseyov, D., Kerem, E., Cohen-Cymberknoh, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

325

EPS6.05 A-STEP: a maximal, incremental, externally paced step test for adults with cystic fibrosis - safety and feasibility testing

Wilson, L.M., Button, B.M., Keating, D., Tarrant, B.J., Corbett, M.D., Young, A., Stirling, R., Wilson, J.W., Lane, R.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

326

IPD1.04 Implementing the International Committee on Mental Health in Cystic Fibrosis (ICMH) Guidelines: practical complexities of managing mental health

Verkleij, M., de Winter, D., Boekhoff, J., Bon, I., Nagelkerke, A.F., Abbott, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

327

IPD2.08 Dose modification of lumacaftor/ivacaftor and the immediate effects on lung function in cystic fibrosis patients with advanced lung disease and 12-month outcomes in this cohort

Popowicz, N., Wood, J., Vekaria, S., Tai, A., Morey, S., Mulrennan, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

328

IPD2.12 Treatment with Orkambi™ in Phe508del homozygous CF patients is associated with improvement in cognition

Wilson, J., Talbot, A., Finlayson, F., Allen-Graham, J., Clark, D., Williams, E., Kotsimbos, T., Keating, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 67 KB

english, 2018

329

P001 Two decades of experience in prenatal diagnosis and carrier screening of cystic fibrosis in Serbia

Radivojevic, D., Minic, P., Lalic, T., Miskovic, M., Dobric, B., Cirkovic, S., Djordjevic, M., Nikolic, R., Djurisic, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 264 KB

english, 2018

330

P002 Importance of population-specific first step CFTR screening in Serbian cystic fibrosis patients

Kusic-Tisma, J., Divac Rankov, A., Ljujic, M., Rakicevic, L., Novkovic, M., Dragicevic, S., Nestorovic, A., Jasnic, J., Radojkovic, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 264 KB

english, 2018

331

P011 Cystic fibrosis newborn screening a Belgian experience

Boboli, H., Boemer, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

332

P018 A bioethical framework for the evaluation of newborn bloodspot screening for cystic fibrosis

Armstrong, R.E., Frith, L., Ulph, F.M., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 75 KB

english, 2018

333

P025 Lumacaftor/ivacaftor in real life for Phe508del homozygous, adolescents with severe and normal lung function

Collet, C., Bui, S., Mittaine, M., Bremont, F., Galode, F., Fayon, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

334

P031 Home registrations of inhalations with tobramycin inhalation powder - the relation between inspiratory flow and cough

Meerburg, J.J., van der Wiel, E.C., Andrinopoulou, E.R., van der Eerden, M.M., Majoor, C.J., Arets, H.G.M., Heijerman, H.G.M., Tiddens, H.A.W.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

335

P042 A 6-year longitudinal population study of Pseudomonas aeruginosa from initial colonisation in the Montpellier CF centre, France

Dupont, C., Benaoudia, M., Chiron, R., Aujoulat, F., Jumas-Bilak, E., Marchandin, H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

336

P062 Surveillance for ototoxicity in children with Mycobacterium abscessus lung disease in a UK cystic fibrosis centre

Palser, S.C., Kaziro, J., Smyth, A.R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

337

P063 Extended SABC incubation for Exophiala species in cystic fibrosis sputa

Looi, E., Geatrix, S., Barry, P.J., Edwards, G., Smith, M., Cullen, M., Brennen, A.L., Jones, A.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

338

P064 Clinical and immunological results of the Berlin Aspergillus Species Study (BASS)

Kaufmann, S., Brandt, C., Nadine, B., Roehmel, J.F., Holz, F., Eschenhagen, P., Mehl, A., Meinus, C., Staab, D., Rickerts, V., Seidel, K., Bacher, P., Hohnstein, T., Scheffold, A., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

339

P065 Berlin Aspergillus Species Study - pet ownership is a risk factor for ABPA in patients with cystic fibrosis

Kaufmann, S., Brandt, C., Barthel, N., Roehmel, J.F., Holz, F., Eschenhagen, P., Mehl, A., Meinus, C., Staab, D., Rickerts, V., Seidel, K., Bacher, P., Hohnstein, T., Scheffold, A., Schwarz, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

340

P069 Changes in airways bacterial community with cystic fibrosis patients’ age and lung function decline

Voronina, O., Ryzhova, N., Kunda, M., Sharapova, N., Aksenova, E., Amelina, E., Shumkova, G., Simonova, O., Egorov, M., Kondratyeva, E., Chuchalin, A., Gintsburg, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

341

P070 Longitudinal analysis of the lower airway microbiota in cystic fibrosis patients during clinical stability compared to those experiencing episodes of pulmonary exacerbation

Einarsson, G.G., Sherrard, L.J., Johnston, E., O'Neill, K., McIlreavey, L., MCGrath, S.J., Gilpin, D.F., Murray, M., Lavelle, G., MCElvaney, G., Boucher, R., Muhlebach, M., Elborn, J.S., Tunney, M.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

342

P071 Predicting the functional intestinal profiles in cystic fibrosis

Coffey, M.J., Nielsen, S., Wemheuer, B., Needham, B., Jaffe, A., Thomas, T., Ooi, C.Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

343

P077 Discontinuation of prophylactic flucloxacillin in young adults with cystic fibrosis

Ravi, K., Snowball, J., Flight, W.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

344

P081 Effect of inhaled ceftazidime on early Burkholderia contaminans lung infection in children with cystic fibrosis

D'alessandro, V., Bettiol, M., Bosch, A., Rentería, F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

345

P092 A service evaluation addressing: are intravenous antibiotics administered at home as clinically effective as intravenous antibiotics administered in hospital in cystic fibrosis patients in the adult cystic fibrosis centre in Aberdeen?

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

346

P095 Intravenous fosfomycin for treatment of pulmonary exacerbations in adult cystic fibrosis patients with chronic infection by Pseudomonas aeruginosa and other Gram-negative bacteria

Messore, B., Bellocchia, M., Bena, C., Biglia, C., Bandelli, G.P., Clivati, E., Bonizzoni, G., Demichelis, S., Traversa, F., Albera, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

347

P097 Role of an exacerbation checklist score in the definition, assessment and outcome of cystic fibrosis pulmonary exacerbations

Addy, C., Bradley, J., Bradbury, I., Elborn, J.S., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

348

P100 Staphyloccocal infection impact on the outcome of lung disease in cystic fibrosis

Smădeanu, E.R., Mosescu, S., Zăpucioiu, C., Ulmeanu, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

349

P101 Clinical data of patients with nontuberculous mycobacteria in a paediatric cystic fibrosis centre in Slovenia

Praprotnik, M., Kotnik Pirš, A., Aldeco, M., Oštir, M., Žolnir Dovč, M., Krivec, U.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 76 KB

english, 2018

350

P103 Clinical effects of omalizumab in adult cystic fibrosis patients with allergic severe asthma associated with allergic bronchopulmonary aspergillosis

Messore, B., Bellocchia, M., Bena, C., Biglia, C., Clivati, E., Bonizzoni, G., Demichelis, S., Traversa, F., Grande, A., Ricciardolo, F.L.M., Albera, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

351

P104 Prevalence, clinical characteristics and outcomes of patients referred to an adult cystic fibrosis centre from pulmonary clinics

Contarini, M., Gramegna, A., Aliberti, S., Sotgiu, G., Colombo, A., Vanoni, N., Amati, F., Pizzamiglio, G., Di Pasquale, M., Dellafiore, S., Pappalettera, M., Colombo, C., Castellani, C., Assael, B.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 72 KB

english, 2018

352

P114 How does the basement membrane change in patients with cystic fibrosis?

Koucký, V., Uhlík, J., Doušová, T., Skalická, V., Pohunek, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

353

P116 Lung function and its association with nutritional and functional status in patients with cystic fibrosis living in the Moscow region

Cherniak, A., Gorinova, Y., Krasovsky, S., Voronkova, A., Mukhina, M., Amelina, E., Kondratyeva, E., Sherman, V., Afanasyeva, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

354

P117 Time course of pulmonary hyperinflation in adult cystic fibrosis: clinical and lung function correlates

Audousset, C., Lohbrunner, A., Prevotat, A., Dhalluin, X., Le Rouzic, O., Wallaert, B., Perez, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

355

P119 An 8-week open-label interventional multi-centre study to evaluate the Lung Clearance Index as endpoint for clinical trials in cystic fibrosis patients ≥6 years of age, chronically infected with Pseudomonas aeruginosa

Welsner, M., Nährig, S., Mellies, U., Sieder, C., Ziegler, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

356

P120 Lung Clearance Index measurement in children with primary ciliary dyskinesia (PCD) and cystic fibrosis; Hacettepe University experience

Emiralioglu, N., Yalcin, E., Oguz, B., Kaplan, M., Tugcu, G., Eryilmaz, S., Gharibzadeh Hizal, M., Dogru, D., Ozcelik, U., Kiper, N.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

357

P123 Lung Clearance Index and vitamin D

Ciuca, I.M., Dediu, M., Vlad, D., Popa, Z., Pop, L.L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

358

P125 An audit of the use of computerised tomography scans for chest imaging in a large UK paediatric cystic fibrosis clinic

Halfhide, C.P., Burrows, E., Harrison, G., Kaleem, M., Southern, K.W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

359

P128 Lung transplantation in paediatric patients with cystic fibrosis: a single centre experience

Spinelli, E., Fazzi, A., Tridello, G., Ocampo Barao, M., Volpi, S., D'orazio, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

360

P135 Improving physiotherapy practice with educational videos

Cobb, K., Nitsche, E., Tinhof, K., Talaska, C., Renner, S., Szepfalusi, Z.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

361

P136 CF@home: feasibility and utility of ear lobe blood gas sampling in the patient's home

Channon, K., Heise, R., Parkinson, H., Reilly, C.C., Perrin, F., Elston, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

362

P139 Vestibular dysfunction and aminoglycoside exposure in cystic fibrosis

Keane, S., Reilly, C.M., Gallagher, C.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

363

P142 Isokinetic evaluation of maximum quadriceps strength (MQS) in 37 CF adult patients

Le Bihan, J., Ramel, S., Paul, H., Cogen, U., Gueganton, L., Verdun, S., Daniel, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

364

P148 Service evaluation of a community exercise programme for people with CF

Haynes, F.A., Cook, M., Sanga, H., Millward, S., Dewar, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

365

P149 Expansion of a leading CF exercise programme: collaborative partnership between a UK health and fitness provider and five UK CF centres

Ahlquist, A.A.A., Douglas, H., Rand, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

366

P153 Service evaluation of an out-patient exercise programme for CF patients

Haynes, F., Mosley, K., Wheedon, K., Dewar, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

367

P157 Role of osteopathic manipulative treatment in cystic fibrosis: a pilot study

Fainardi, V., Benecchi, S., Longo, F., Tripodi, M.C., Villani, M.L., Teopompi, E., Chetta, A.A., Pisi, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

368

P161 The Cystic Fibrosis-Related Diabetes (CFRD) self-management triad – it is about more than just numbers

Collins, S., Jones, A., Woodward, S., Sturt, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

369

P162 The relationship of Cystic Fibrosis-Related Diabetes (CFRD) and abnormal lipid profiles in adults with cystic fibrosis

Caskey, S., Lynch, V., Addy, C., Mccaughan, J., Downey, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

370

P164 How can continuous glucose monitoring system impact on therapy of Cystic Fibrosis-Related Diabetes (CFRD) in youth

Todorovic, S., Milenkovic, T., Minic, P., Mitrovic, K., Sovtic, A., Rodic, M., Rade, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

371

P172 Colorectal cancer in adults with cystic fibrosis: our experience at the All Wales Adult Cystic Fibrosis Centre

Sayers, A., Turner, J., Speight, L., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

372

P174 Faecal calprotectin in cystic fibrosis patients during respiratory exacerbation

Schnapp, Z., Livnat-Levanon, G., Shteinberg, M., Hartman, C., Elenberg, Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

373

P184 Factors influencing total serum cholesterol in cystic fibrosis children and adolescents - preliminary data

Mielus, M., Surowiecka, M., Oltarzewski, M., Sands, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

374

P192 To be or not to be (happy): fat is the question?

Proud, D., Ketchell, R.I., Lau, D., Rezaie, M., Speight, L., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

375

P194 Evaluating the effectiveness of dietetic interventions: developing a dietetic outcome measures tool for cystic fibrosis

Cave, L., Bartlett, F., Fox, R., Lowdon, J., Mccabe, H., Snowball, J., Thornton, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

376

P195 Relationship between nutritional status and pulmonary function in adults with cystic fibrosis: cross-sectional and longitudinal analyses

Hollander, F.M., Roelofs, J., de Roos, N.M., Heijerman, H.G.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

377

P202 How well do children with CF grow in a CF-centre in Sweden when no newborn screening exists, but an old tradition with physical activity as the baseline treatment?

Nilsson, M., Björkman, K., Hansen, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

378

P206 Putting some backbone into managing low vitamin D

Proud, D., Ketchell, R.I., Lau, D., Rezaie, M., Lea-Davies, M., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

379

P207 The influence of genetic factors and phenotype on the development of vitamin D deficiency in children with cystic fibrosis

Zhekaite, E., Kondratyeva, E., Voronkova, A., Sherman, V., Nikonova, V., Ershova, E., Kostyuk, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 67 KB

english, 2018

380

P208 Vitamin D Deficiency in patients with cystic fibrosis: are we adhering to monitoring recommendations?

Jacob, S., Carlin, K., Hutchinson, D., Nagel, A., O'brien, C., Bhandari, N., Payakachat, N., Rosenfeld, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

381

P209 Monitoring bone health in the All Wales Adult CF Centre (AWACFC)

Wilson, C., Speight, L., Ketchell, R., Petit, R., Lau, D., Stone, M., Farmer, B., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

382

P215 Age at menarche in girls with cystic fibrosis

Tournier, A., Mittaine, M., Cartault, A., Bournez, M., Munzer, C., Murris, M., Vaysse, C., Brémont, F., Tauber, M., Pienkowski, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

383

P221 Home intravenous antibiotics: behind closed doors

Smith, A., Hopkins, A.L., Ketchell, R.I., Duckers, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

384

P224 Aseptic centralised versus home extemporaneous preparation for cystic fibrosis outpatients’ parenteral antibiotic therapy: a survey on nurses’ satisfaction

Garcia, S., Margueritte, L., Carpentier, I., Nave, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

385

P227 Using poetry to teach students and others about CF

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

386

P237 Views of healthcare professionals on patients having access to their secondary care electronic healthcare record: results of a cross-sectional questionnaire

Sawant, A.P., Chadwick, H., White, H., Spoletini, G., Whitaker, P., Etherington, C., Clifton, I., Lee, T., Duff, A.J., Peckham, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

387

P238 The use of an online learning module (LearnPro NHS TM ) to educate and assess staff working in cystic fibrosis care

Mallinson, A.M., Mcgrath, A.J., Marwick, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

388

P252 When doctors go to patients: a patient-based evaluation of the CFQ

Coucke, R., Bontemps, V., Hayes, K., De Carli, P., Hjelte, L., Hollander, A., Sermet-Gaudelus, I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

389

P258 Searching for CFTR mutations in healthy children and CF paediatric patients from Russian populations

Zinchenko, R.A., Petrova, N.V., Vasilyeva, T.A., Kondratyeva, E.I., Voronkova, A.Y., Sherman, V.D., Ginter, E.K., Kashirskaya, N.Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

390

P260 Searching for CFTR mutations in CF patients from North Ossetia-Alania Republic, Russian Federation

Vasilyeva, T.A., Petrova, N.V., Kashirskaya, N.Y., Getoeva, Z.K., Dzhadzhieva, M.Y., Novoselova, O.G., Kondratyeva, E.I., Ginter, E.K., Zinchenko, R.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

391

P261 Data from the Cystic Fibrosis Patient Registry of the Russian Federation (comparison 2011 and 2016)

Kashirskaya, N.Y., Krasovskiy, S.A., Kondratyeva, E.I., Amelina, E.A., Voronkova, A.Y., Chernyak, A.V., Gembitskaya, T.E., Sherman, V.D., Ulyanova, L.V., Alimova, I.L., Novikova, O.B., Vasilyeva, E.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 62 KB

english, 2018

392

P264 Analysis of demographic characteristics and cumulative survival of cystic fibrosis population in the Republic of Macedonia

Fushtik, S., Spirevska, L., Jakovska, T., Nakov, Z.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

393

P266 Early clinical determinants of respiratory outcome in patients with cystic fibrosis

Williams, T.P., Zarska, K., Thia, L.P., Forton, J.T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

394

P267 Pulmonary exacerbations and risk of death amongst patients with cystic fibrosis (CF) with homozygous and heterozygous F508del mutations in Ireland

Kirwan, L., Fletcher, G., Harrington, M., Zhou, S., Jeleniewska, P., Hassan, M., Rubin, J., Jackson, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

395

P274 I'm with the band

Aldous, G., Frost, F., Pinnock, N., Walshaw, M., Nazareth, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

396

P275 The prespectives of Canadian cystic fibrosis pharmacists and patients on the role of the cystic fibrosis pharmacist in an outpatient multidisciplinary care team

Lautrup, K.R., Mctaggart, N.K., Spina, S.P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

397

P277 Cystic fibrosis sub-speciality training: will supply meet demand?

Griffiths, P., Brockelsby, C., Frost, F., Nazareth, D., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

398

Author Index

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 798 KB

2018

399

P170 Differences in clinical outcomes of paediatric cystic fibrosis patients with and without meconium ileus

Tan, J., Coffey, M.J., Ooi, C.Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 63 KB

english, 2018

400

WS06.6 Effect of lumacaftor/ivacaftor on lung clearance index and exercise capacity among patients aged over 12 years with cystic fibrosis homozygous for F508del-CFTR

Hatziagorou, E., Kouroukli, E., Parisi, M., Kampouras, A., Nousia, L., Tsanakas, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

401

WS10.4 Evaluating cystic fibrosis newborn screening diagnostic performance in the United States

McColley, S.A., Sontag, M., Elbert, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 68 KB

english, 2018

402

WS11.3 GVF27, HVA36 and IMY47: human-derived host defence peptides for alternative cystic fibrosis therapeutic intervention strategies

Bosso, A., Gaglione, R., Pane, K., Cafaro, V., Arciello, A., Notomista, E., Pizzo, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

403

WS13.5 Assessment of the prevalence and severity of urinary and ano-rectal functional disorders and their impact on quality of life and sexuality in adult with cystic fibrosis in the French North-West Cystic Fibrosis Network

Ramel, S., Gueganton, L., Troussier, F., Markov, M., Danner, I., Loppinet, V., Belleguic, C., Berhault, I., Huge, S., Fretay, R., Mankikian, J., Payet, A., Maillot, A., Le Bihan, J., Hubeaux, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

404

WS14.6 Demographics of patients in a phase 2 trial of acebilustat in patients with cystic fibrosis (EMPIRE CF)

Elborn, J.S., Ahuja, S., Mershon, J., Springman, E., Rowe, S.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

405

WS15.4 First functional characterisation of the R751L CFTR mutation using an ex vivo primary airway epithelial cell culture model

Haq, I.J., Gardner, A.I., Saint-Criq, V., Thomas, M.F., Townshend, J., Ben-Hamida, M., O'brien, C., Ward, C., Gray, M., Brodlie, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

406

WS18.2 The transition towards lung transplant for cystic fibrosis in the United Kingdom

West, N.E., Francis, C.J., Medhurst, N.D., Thaxton, A.L., Tallarico, E., Cosgriff, R., Dunk, R., Brownlee, K.G., Elborn, J.S., Bush, E.L., Shah, P.D., Merlo, C.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

407

WS18.6 Pregnancy after lung transplantation in cystic fibrosis patients

Rönsholt, F.F., Philipsen, L.K., Pressler, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

408

EPS1.04 Use of ex vivo paediatric primary nasal epithelial cultures to investigate TMEM16A as a potential therapeutic target in children with cystic fibrosis

Haq, I.J., Verdon, B., Jiwa, K., Saint-Criq, V., Gardner, A.I., Ward, C., Gray, M., Brodlie, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 64 KB

english, 2018

409

EPS2.02 Influence phase 1 xenobiotics metabolism genes on the efficiency of antibacterial therapy in patients from the Russian Federation and the Republic of Belarus

Kondratyeva, E.I., Novoselova, O., Petrova, N., Chakova, N., Krasovskii, S., Voronkova, A., Sherman, V., Bobrovnichy, V., Melyanovskaya, Y., Zinchenko, R., Kutsev, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

410

EPS2.03 The influence of polymorphism of metalloproteinase genes on the formation of CF-liver cirrhosis and CF pneumofibrosis

Goryainova, A., Kashirskaya, N., Belmer, S., Semykin, S.Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

411

EPS4.03 Clinical implications of the cystic fibrosis airway microbial metagenome

Gessner, M., Pienkowska, K., Moran Losada, P., Hedtfeld, S., Dorda, M., Wiehlmann, L., Tümmler, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

412

EPS4.07 Interactions of Pseudomonas aeruginosa with other bacterial species in an artificial sputum model

Wright, L.L., Chatterley, L., Walshaw, M., Ledson, M., Greenwood, J., Nazareth, D., O'brien, S., Winstanley, C., Fothergill, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

413

EPS5.06 Demography and clinical outcomes in cystic fibrosis lung transplant recipients in Belgium

Thomas, M., Wanyama, S., Dupont, L., Etienne, I., Evrard, P., Rondelet, B., Sokolow, Y., Van Raemdonck, D.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

414

P013 Selection of a genetic test for neonatal screening of cystic fibrosis in the mixed population of Luxembourg

Kulisic, M., Denine, I., de la Barrière, H., Fellmann, F., Schlesser, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 54 KB

english, 2018

415

P024 Effects of food and moderate hepatic impairment on the pharmacokinetics (PK) of tezacaftor/ivacaftor (TEZ/IVA)

Viswanathan, L., Lekstrom-Himes, J., Garg, V., Agarwal, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

416

P044 Azithromycin resistance develops fast in P. aeruginosa but has no negative impact on lung function development in CF patients with chronic infection

Arge, O., Høiby, N., Hansen, C.R., Johansen, U.R., Pressler, T., Skov, M., Jelsbak, L., Ciofu, O.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

417

P046 Relationship between the first isolation of Pseudomonas Aeruginosa and the preceding viral infection in children with cystic fibrosis

Shaltoni, D., Narayan, O.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 57 KB

english, 2018

418

P054 Human reservoirs of pathogens colonising the airways of cystic fibrosis patients

Sandri, A., Cazzarolli, C., Burlacchini, G., Melotti, P., Volpi, S., D'orazio, C., Lleo, M.M., Signoretto, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

419

P056 Macrophage activation syndrome due to Nocardia in a cystic fibrosis patient

Sismanlar Eyuboglu, T., Aslan, A.T., Ramaslı Gursoy, T., Kocak, U., Aktas Tapısız, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

420

P113 Plasma sphingomyelin and ceramide levels of cystic fibrosis patients

Bal Topçu, D., Tuğcu, G., Er, B., Özcan, F., Aslan, M., Esref, S., Hizal, M., Yalçın, E., Doğru Ersöz, D., Çöplü, L., Özçelik, U., Kiper, N., Lay, İ., Öztaş, Y.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 61 KB

english, 2018

421

P115 Risk factors for early lung function decline in young children with cystic fibrosis

Teper, A., Balinotti, J., Rodriguez, V., Lubovich, S., Zaragoza, S., Chang, D., Escobar, N., Galanternik, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 75 KB

english, 2018

422

P124 Bicarbonate and oxygen saturation predict the need for fitness to fly test in patients with cystic fibrosis

Spoletini, G., Sawant, A., Etherington, C., Watts, S., Clifton, I., Whitaker, P., Peckham, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

423

P133 Re-audit of the UK ACPCF Physiotherapy National Standards of Care

Morrison, L., Duncan, N.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 63 KB

english, 2018

424

P138 Sampling methods used in non-expectorating children ≤3 years of age with cystic fibrosis in a London CF centre

Miller, J., O'connor, R., Pao, C.S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

425

P141 The impact of exacerbations on muscle force, exercise capacity and quality of life in adults with cystic fibrosis

Pyl, F., Van Braeckel, E., De Baets, F., Calders, P., Bernaert, S., Declercq, D., Van Biervliet, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

426

P152 Cardiopulmonary exercise test and lumacaftor/ivacaftor in cystic fibrosis

Philipsen, L.K.D., Pressler, T.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

427

P154 An interim service evaluation of APP-based individual exercise programmes which are remotely monitored and progressed by a clinical physiologist specialising in exercise from a large Adult Cystic Fibrosis Centre

Waller, I.W., Johnson, S.C., Mcvean, R., Webb, A.K., Barry, P.J., Jones, A.M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

428

P160 Striking the balance between cystic fibrosis and Cystic Fibrosis-Related Diabetes (CFRD) - a meta-ethnography

Collins, S., Jones, A., Woodward, S., Sturt, J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

429

P173 Lactase activity in small intestinal biopsies in children with CF

Roslavtseva, E., Gordeeva, I., Simonova, O., Lokhmatov, M., Namazova-Baranova, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

430

P181 Vitamin E supplementation with fat soluble formulation in children with cystic fibrosis: two years’ follow-up

Roda, J., Maia, C., Silva, A.R., Almeida, S., Ferreira, R.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

431

P193 Cost analysis of the treatment of exacerbations in children with CF depending on nutritional status

Maksimycheva, T., Kondratyeva, E., Budzinskiy, R., Zhekayte, E., Voronkova, A., Sherman, V.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 73 KB

english, 2018

432

P204 An increase in weight and fat mass observed following five months of ivacaftor treatment plateaus at 24 months in adults with G551D-related cystic fibrosis

Tierney, A., King, S.J., Edgeworth, D., Williams, E., Finlayson, F., Keating, D., Clark, D., Button, B.M., Kotsimbos, T., Wilson, J.W.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

433

P217 Cystic fibrosis with pancreatic insufficiency is associated with a high incidence of subfertility in women

Shteinberg, M., Ben Lulu, A., Downey, D., Blumenfeld, Z., Rousset-Jablonski, C., Percival, M., Colombo, A., Stein, N., Livnat, G., Gur, M., Bentur, L., Mussaffi, H., Blau, H., Sarouk, I., Efrati, O.,

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

434

P220 Pharmacist consultation introduced to annual review of adults with cystic fibrosis

Smith, M., Takawira, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 50 KB

english, 2018

435

P225 Support to self-esteem building among children aged 6 to 10 years old: “My little notebook that makes me feel better”

Leger, P., Kerbrat, M., Llerena, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

436

P241 Why won't children keep exercising? Barriers and facilitators to exercise and physical activity maintenance - a qualitative study

Douglas, H., Rand, S., Denford, S., Bryon, M., Main, E.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

437

P243 Evaluation of youth work support for teenagers and young adults with cystic fibrosis

Mehmood, A., Cammidge, S., Guy, E., Peckham, D., Duff, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

438

WS03.2 The effect of an intensive residential rehabilitation program with adjusted nutritional care on body composition in adult patients with cystic fibrosis

Buts, S., Dereeper, S., Würth, B., Franckx, H., De Guchtenaere, A., Van Biervliet, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

439

EPS6.07 Effects of physical retraining on the body composition of adult patients with cystic fibrosis

Godin, J., Bernard, H., Perez, T., Le Rouzic, O., Wallaert, B., Prevotat, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 64 KB

english, 2018

440

IPD1.08 Treating unresolved grief in parents of children with cystic fibrosis

Branch-Smith, C., Barrett, A., Balding, E., Grover, Z., Yikilmaz, G., Bourke, C., Depiazzi, J., Sander, N., Foster, J., Zepf, F., Schultz, A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

441

P091 Midline administration of aminoglycoside antibiotics is safe in adult cystic fibrosis patients

Macduff, N., Sammons, L., Macduff, A., Thickett, K.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

442

P169 Improved clinical outcomes following Nissen fundoplication in cystic fibrosis patients: experience in a large adult CF centre

Sivabalah, K., Frost, F., Greenwood, J., Walshaw, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

443

WS07.4 Bereavement and loss in a 14 year-old girl and the impact on CF

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 64 KB

english, 2018

444

EPS2.01 Association of polymorphic variants of GSTT1, GSTM1, GSTP1 and GCLC genes with the severity of the cystic fibrosis clinical manifestations

Novoselova, O., Petrova, N.V., Krasovskiy, S.A., Kondratieva, E.I., Chakova, N.N., Bobrovnichy, V.I., Voronkova, A.Y., Sherman, V.D., Melyanovskaya, Y.L., Zinchenko, R.A.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 80 KB

english, 2018

445

IPD1.05 Instituting mental health screening in a Canadian paediatric cystic fibrosis clinic

Gravelle, A., Kolb, T., Jenkins, S., Mcmahon, V., Chilvers, M.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

446

P159 Usefulness of extended oral glucose tolerance test in patients with cystic fibrosis older than 16 years

Baran, E., Godoy, A., Merino, E., Benigni, L., Gonzalez, J., Pierini, N., Copparoni, G., Farah, A., Zubillaga, M., Rivera, A., Ferranti, S., Bocanegra, R., Lorenzin, A., Barrena, E., Varela, C., Gatti

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018

447

EPS6.02 Investigating the experience of adults with cystic fibrosis using long-term domiciliary non-invasive ventilation

Choyce, J., Hewison, A., Swift, A., Whitehouse, J.L., Rashid, R., Nash, E.F.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 51 KB

english, 2018

448

WS04.6 Balancing the immune response in cystic fibrosis: using zebrafish models of inflammation to uncover new therapeutic approaches

Bernut, A., Floto, A., Renshaw, S.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 71 KB

english, 2018

449

The open door policy - An important and under-recognised activity of the adult CF centre

Tai, Anna Sze, Morey, Sue

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 118 KB

english, 2018

450

News

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 1.07 MB

english, 2018

451

EPS4.02 Porphyromonas, a candidate biomarker for detection of Pseudomonas aeruginosa pulmonary infection in cystic fibrosis

Guilloux, C.-A., Marenne, G., Mondot, S., Lamoureux, C., Billard, L., Gouriou, S., Vallet, S., Le Berre, R., Férec, C., Génin, E., Héry-Arnaud, G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 59 KB

english, 2018

452

News

Wilschanski, Michael

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 191 KB

english, 2018

453

EPS1.03 Human respiratory epithelial cells prevent Aspergillus fumigatus germination

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 288 KB

2018

454

WS08.3 Combined ramp and supramaximal cardiopulmonary exercise testing for individuals with cystic fibrosis

Saynor, Z.L., Causer, A.J., Allenby, M.I., Carroll, M., Connett, G., Daniels, T., Shute, J.K., Cummings, M.H., Shepherd, A.I.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 55 KB

2018

455

EPS1.03 Human respiratory epithelial cells prevent Aspergillus fumigatus germination

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 288 KB

english, 2018

456

P254 Impact of cystic fibrosis on healthy siblings: a systematic review

Chudleigh, J., Browne, R., Radbourne, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

457

P254 Impact of cystic fibrosis on healthy siblings: a systematic review

Chudleigh, J., Browne, R., Radbourne, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 56 KB

2018

458

Editorial Board

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 60 KB

english, 2018

459

P033 A twinned remote program of supervised adapted physical activity (APA) for French & Irish people living with cystic fibrosis improves self- reported physical activity level and physical fitness

Desplanche, E., Harnett, P., Varray, A., Herbinet, A., Chiron, R., Thöni, G., Casserly, B.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 56 KB

english, 2018

460

P066 Aspergillus fumigatus degrades the respiratory mucins MUC5B and MUC5AC

Cowley, A.C., Horsley, A., Bignell, E., Denning, D.W., Thornton, D.J.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

461

P212 Cardiovascular risk in an adult CF population: a 10-year retrospective analysis

Greig, N.J., White, H., Chadwick, H.K., Cartwright, A., Peckham, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 66 KB

english, 2018

462

P010 The efficiency of CF newborn screening for homozygous F508del patients

Sherman, V., Kondrateva, E., Voronkova, A., Kashirskaya, N., Zhekayte, E., Shabalova, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 70 KB

english, 2018

463

P048 “Dr Dog” will see you now? First steps in assessing the utility of trained sniffer dogs to detect Pseudomonas aeruginosa ( Pa ) airway infection in non-expectorating CF patients

Davies, J.C., Alton, E.W., Simbo, A., Murphy, R., Seth, I., Williams, K., Jolly, L., Morant, S., Guest, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 72 KB

english, 2018

464

EPS3.05 GLPG2222 in subjects with cystic fibrosis homozygous for F508del: results from a phase II study (FLAMINGO)

van der Ent, K.C., Minic, P., Verhulst, S., Van Braeckel, E., Flume, P., Boas, S., Geller, D., de Kock, H., Loyau, S., Muller, K., Kanters, D., Conrath, K., Van de Steen, O.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 55 KB

english, 2018

465

P143 A multidimensional analysis of exercise capacity amongst adults with cystic fibrosis

Buckley, R., Cunningham, C., Lennon, O., Blake, C., Gallagher, C.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 53 KB

english, 2018

466

P027 Alteration of lipid epoxy metabolites due to CFTR modulation with lumacaftor/ivacaftor in df508del homozygous patients

Roehmel, J.F., Staab, D., Specht, P., Schwarz, C., Rothe, M., Schebb, N.H., Weylandt, K.H.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 58 KB

english, 2018

467

P212 Cardiovascular risk in an adult CF population: a 10-year retrospective analysis

Greig, N.J., White, H., Chadwick, H.K., Cartwright, A., Peckham, D.G.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 66 KB

2018

468

P010 The efficiency of CF newborn screening for homozygous F508del patients

Sherman, V., Kondrateva, E., Voronkova, A., Kashirskaya, N., Zhekayte, E., Shabalova, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 70 KB

2018

469

P048 “Dr Dog” will see you now? First steps in assessing the utility of trained sniffer dogs to detect Pseudomonas aeruginosa ( Pa ) airway infection in non-expectorating CF patients

Davies, J.C., Alton, E.W., Simbo, A., Murphy, R., Seth, I., Williams, K., Jolly, L., Morant, S., Guest, C.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 72 KB

2018

470

EPS3.05 GLPG2222 in subjects with cystic fibrosis homozygous for F508del: results from a phase II study (FLAMINGO)

van der Ent, K.C., Minic, P., Verhulst, S., Van Braeckel, E., Flume, P., Boas, S., Geller, D., de Kock, H., Loyau, S., Muller, K., Kanters, D., Conrath, K., Van de Steen, O.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 55 KB

2018

471

P105 Clinical outcomes associated with infected totally implantable venous access devices

Lee, X., Frost, F., Greenwood, J., Brockelsby, C., Naylor, T., Shah, R., Griffiths, P.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Fichier:

PDF, 54 KB

2018

472

EPS3.01 Transduction of rhesus macaque lung following repeat dosing by adeno-associated virus serotype 1

Yanda, M.K., Wang, H., Guggino, W.B., Cebotaru, L.

Journal:

Journal of Cystic Fibrosis

Année:

2018

Langue:

english

Fichier:

PDF, 52 KB

english, 2018