Galactonojirimycin derivatives restore mutant human β-galactosidase activities expressed in fibroblasts from enzyme-deficient knockout mouse
Lika Tominaga, Yoshimi Ogawa, Megumi Taniguchi, Kousaku Ohno, Junichiro Matsuda, Akihiro Oshima, Yoshiyuki Suzuki, Eiji NanbaVolume:
23
Année:
2001
Langue:
english
DOI:
10.1016/s0387-7604(01)00216-9
Fichier:
PDF, 91 KB
english, 2001